[Severe pulmonary arterial hypertension and primary antiphospholipid antibodies syndrome]. / Ipertensione arteriosa polmonare severa e sindrome da anticorpi antifosfolipidi primaria.

A young patient with severe pulmonary hypertension of thromboembolic origin due to recurrent deep vein thrombosis is described. Although he presented no signs of systemic lupus erythematous, a high quantity of cardiolipin antibodies was found in his serum. Therefore, we discuss a possible association between the primary antiphospholipid antibodies syndrome and pulmonary embolic events.