Subject(s)
Hemangioma/congenital , Laryngeal Diseases/etiology , Respiratory Sounds , Humans , LaryngismusSubject(s)
Pneumopericardium/etiology , Child , Humans , Male , Pneumopericardium/diagnostic imaging , Radiography , UltrasonographyABSTRACT
We describe a 6-year-old boy with solitary rectal ulcer syndrome, and the sigmoidoscopic and histopathologic findings. The evolution of the histologic features and the absence of trauma suggest that the origin of the ulceration is ischemic in nature.
Subject(s)
Gastrointestinal Hemorrhage/pathology , Rectal Diseases/pathology , Child , Humans , Male , Syndrome , Ulcer/pathologySubject(s)
Hepatitis A/immunology , Hepatitis Antibodies/blood , Hepatovirus/immunology , Immunoglobulin M/blood , Adolescent , Child , Female , Hepatitis A Antibodies , Humans , Male , Recurrence , Time FactorsABSTRACT
Twelve patients with congenital hepatic fibrosis have been retrospectively studied and followed for 1 to 14 years. Clinical features, hepatic function tests and biopsy have been analyzed. Presence of portal hypertension and congenital malformation have been investigated. Clinical presentations varies from newborn to nine years of age without male or female predominance. Most frequent clinical form has been hypertensive type. Cholangitic type has worse prognosis. Familiar recurrence rate is 20%. Congenital malformations are associated in 92% most frequently infantile polycystic kidney disease. Hepatic biopsy has confirmed diagnosis in all patients.
