Subject(s)
Aneurysm, False/congenital , Aortic Valve/abnormalities , Heart Aneurysm/congenital , Heart Defects, Congenital , Mitral Valve/abnormalities , Aneurysm, False/diagnostic imaging , Aneurysm, False/physiopathology , Aortic Valve/diagnostic imaging , Aortic Valve/physiopathology , Child, Preschool , Echocardiography, Doppler, Color , Echocardiography, Three-Dimensional , Female , Heart Aneurysm/diagnostic imaging , Heart Aneurysm/physiopathology , Heart Defects, Congenital/diagnostic imaging , Heart Defects, Congenital/physiopathology , Humans , Infant , Mitral Valve/diagnostic imaging , Mitral Valve/physiopathology , Prognosis , Tomography, X-Ray ComputedABSTRACT
Ebstein's anomaly is a rare congenital heart defect. Associated lesions are uncommon, and the mortality rates can be as high as 54% during the first month of life. Two cases of severe Ebstein's anomaly with ventricular septal defect are described. It is speculated that this rare association, allowing adequate forward pulmonary blood flow in the neonate, permitted the reported patients to survive the neonatal period, which is the most life-threatening time. The authors propose that the presence of a small ventricular septal defect can be beneficial for such patients, averting the need for surgery during early infancy when the risk is highest.
Subject(s)
Ebstein Anomaly/epidemiology , Heart Septal Defects, Ventricular/epidemiology , Comorbidity , Coronary Circulation , Ebstein Anomaly/blood , Ebstein Anomaly/diagnostic imaging , Ebstein Anomaly/physiopathology , Electrocardiography , Female , Heart Septal Defects, Ventricular/blood , Heart Septal Defects, Ventricular/diagnostic imaging , Heart Septal Defects, Ventricular/physiopathology , Humans , Infant , Oxygen/blood , UltrasonographyABSTRACT
Early postoperative localized cardiac tamponade occurred in a 4-month old infant after ventricular septal defect repair. The clinical findings were as for acute superior vena cava syndrome. The diagnosis was accurately made using echocardiography and measurement of the superior vena cava and right atrial pressure. Surgical revision was necessary to remove a large clot from the superior vena cava-right atrium junction.
Subject(s)
Cardiac Tamponade/etiology , Heart Septal Defects, Ventricular/surgery , Superior Vena Cava Syndrome/etiology , Cardiac Tamponade/diagnosis , Cardiac Tamponade/surgery , Echocardiography, Doppler , Female , Follow-Up Studies , Heart Septal Defects, Ventricular/diagnosis , Humans , Infant , Postoperative Complications/diagnosis , Reoperation , Superior Vena Cava Syndrome/diagnosis , Superior Vena Cava Syndrome/surgery , Treatment OutcomeABSTRACT
A 64 year old man presented with a traumatic ventricular septal defect following blunt chest trauma 40 years before. Echocardiography and left ventriculography were helpful in locating the unusual septal defect, which was subpulmonary. The shunt was small, but the anomalous chronic overload led to right ventricular failure. The surgical correction was thus too late to improve right ventricular function.
