Subject(s)
Humans , Female , Middle Aged , Constipation/complications , Constipation/diagnosis , Colectomy/methods , Intestinal Pseudo-Obstruction , Intestinal Pseudo-Obstruction/surgery , Megacolon/complications , Megacolon/surgery , Megacolon , Intestinal Pseudo-Obstruction/complications , Immunohistochemistry/methods , ImmunohistochemistryABSTRACT
Congenital pseudoarthrosis of the tibia (CPT) is an uncommon disease presenting a tibial nonunion since birth and frequently associated to neurofibromatosis type 1. Surgical management by wide excision of the pseudoarthrosis and sustitution of the defect with vascularized bone in an early stage has proven to be the most effective technique in terms of bone consolidation. We present a clinical case of a 22-month-old patient with CPT treated successfully by reconstruction with a free vascularized fibula graft with an excellent functional result.
Subject(s)
Fibula/blood supply , Fibula/transplantation , Pseudarthrosis/congenital , Pseudarthrosis/surgery , Tibia/surgery , Humans , Infant , MaleABSTRACT
La pseudoartrosis congénita de tibia (PCT) es una enfermedad rara consistente en un tipo específico de falta de unión presente desde el nacimiento asociada frecuentemente a neurofi bromatosis tipo 1. En el manejo quirúrgico es la resección amplia del foco de pseudoartrosis y sustitución del defecto con tejido óseo vascularizado que, realizado de manera precoz, ha demostrado ser la técnica más efectiva en términos de consolidación ósea. Presentamos un caso clínico de un paciente de 22 meses de edad con PCT que fue tratado con éxito mediante reconstrucción con injerto libre vascularizado de peroné, presentando un excelente resultado funcional (AU)
Congenital pseudoarthrosis of the tibia (CPT) is an uncommon disease presenting a tibial nonunion since birth and frequently associated to neurofi bromatosis type 1. Surgical management by wide excision of the pseudoarthrosis and sustitution of the defect with vascularized bone in an early stage has proven to be the most effective technique in terms of bone consolidation. We present a clinical case of a 22-month-old patient with CPT treated successfully by reconstruction with a free vascularized fibula graft with an excellent functional result (AU)
