ABSTRACT
We describe a patient with a chronic acquired predominantly motor polyneuropathy. His clinical picture initially led to a diagnosis of lower motor neuron form of amyotrophic lateral sclerosis. However electrophysiological examination revealed multifocal, prevalently proximal, conduction blocks at sites not prone to compression. Distinguishing this unusual polyneuropathy from motor neuron diseases is critical, since the former is a potentially, treatable disorder.
Subject(s)
Demyelinating Diseases/diagnosis , Motor Neurons , Neuromuscular Diseases/diagnosis , Adult , Amyotrophic Lateral Sclerosis/diagnosis , Demyelinating Diseases/physiopathology , Diagnosis, Differential , Humans , Male , Median Nerve/physiopathology , Neural Conduction , Neurologic ExaminationABSTRACT
We describe a patient having serologically confirmed Borrelia burgdorferi infection manifesting meningoencephalomyeloradiculoneuritis. The clinical and MRI features suggested a multifocal vascular nervous system involvement. EMG-ENG showed abnormalities consistent with axonal degeneration initially involving the more proximal segments of the lower limb nerves.
Subject(s)
Lyme Disease/complications , Magnetic Resonance Imaging , Meningoencephalitis/etiology , Humans , Male , Meningoencephalitis/diagnosis , Meningoencephalitis/physiopathology , Middle AgedABSTRACT
A case of idiopathic Fahr's disease with interesting clinical and neuroradiological findings is described. The nosological identity and the pathogenetic factors of this complex condition are discussed.
