ABSTRACT
Medulloepithelioma of the ciliary body is an uncommon intraocular tumor occurring during the first year of life. Malignant degeneration may occur. We report the case of a 4-year-old child who presented medulloepithelioma of the left eye disclosed by oesotropia at 2 years of age. Clinically, there was oesotropia, positive light perception and cataract with vascular membrane spreading to the nasal side of the irido-corneal angle. CT scan and ultrasound B revealed a ciliary body tumor involving the sclera and orbital fat. After exenteration, the pathology study reported malignant medulloepithelioma of the ciliary body with scleral extension. No local recurrence or metastasis has been observed at 8 months follow-up. We discuss the clinical, radiological and therapeutic features of this uncommon tumor.
Subject(s)
Ciliary Body , Neoplasms, Neuroepithelial/congenital , Uveal Neoplasms/congenital , Child, Preschool , Ciliary Body/pathology , Ciliary Body/surgery , Eye Enucleation , Follow-Up Studies , Humans , Infant , Male , Neoplasms, Neuroepithelial/diagnosis , Neoplasms, Neuroepithelial/pathology , Neoplasms, Neuroepithelial/surgery , Tomography, X-Ray Computed , Ultrasonography , Uveal Neoplasms/diagnosis , Uveal Neoplasms/pathology , Uveal Neoplasms/surgeryABSTRACT
We report a patient with odontogenic myxoma of the upper maxillary. The authors underline for this particular case, that there are no clinical features specific of the tumor; the diagnosis can be only histological. The evolution of this tumor is always benign.
