ABSTRACT
Ewing's sarcoma is generally an aggressive, poorly differentiated bone and soft tissue tumor affecting children and young adults, it accounts for 4%-6% of all primary bone tumors and primary facial locations occur in only 1%-4% of all cases, primarily in the mandible and calvaria. Involvement of the paranasal sinuses is rare. Here we report the case of an 11-year-old girl with no medical, surgical, or traumatic history, who presented for 1 month and progressive evolution of swelling of the left cheek, associated with pain, nasal obstruction, rhinorrhea, and a slight weight loss not quantified. A craniofacial computed tomography (CT) scan showed a mixed lytic and condensing lesional tissue process centered on the left maxillary sinus, heterogeneously enhanced after contrast injection, lysing the walls of the sinus extended to the homolateral nasal cavity and slightly infiltrating the adjacent soft tissues. An incisional biopsy was performed and the pathological study proved that it was Ewing's sarcoma. She was put on neoadjuvant chemotherapy using 6 courses of vincristine, doxorubicin, ifosfamide, etoposide which resulted in a partial regression of the tumor size by 50%. Then the patient was put on combined chemotherapy and radiotherapy. A follow-up CT scan after 6 courses of vincristine, actinomycin, cyclophosphamide, and 17 sessions of radiotherapy showed lesion stability. Maxillary Ewing's sarcoma is a rare and aggressive tumor. Therefore, early diagnosis, combination therapy, and long-term follow-up are suggested in such cases to improve the survival rate.
ABSTRACT
Ollier disease is an uncommon disease characterized by several enchondromas and an asymmetric distribution of cartilage lesions, which can vary significantly in size, location, age, and gender. The primary symptom of this condition is a nonossifying chondrocyte mass or hamartomatous chondrocyte growth in the metaphysis of a short or long bone. Specific cases can progress to chondrosarcoma or osteosarcoma. X-ray is the most fundamental diagnostic technique for skeletal illnesses. In this article, we present a case of Ollier disease from Mother and Child Hospital IBN SINA, Rabat, Morocco.
ABSTRACT
Congenital bilateral perisylvian syndrome, also known as bilateral periopercular syndrome or perisylvian polymicrogyria, is an exceptionally rare neurological disorder characterized by homogeneous clinicoradiological symptoms. There are consequently wide spectrums of clinical manifestations. In perisylvian syndrome. MRI is the preferred imaging technique. We describe the case of a female 8-year-old child who has a history of generalized tonic-clonic seizures. and was identified to have bilateral perisylvian syndrome based on MR imaging findings.
ABSTRACT
Solitary fibrous tumors of the pleura are rare mesenchymal tumors. The diagnosis is often made incidentally. We report the case of 65 year old patient consulting for dry cough evolving for 1 year. The clinical examination revealed a mattness of the right hemi thorax. The chest X-ray detected a right lower lobar opacity. The CT scan showed a right lateral basal mass, connected at an obtuse angle with the wall. A CTguided biopsy with an anatomopathological and immunohistochemical examination were performed, thus confirming the diagnosis of a solitary fibrous pleural tumor. The evolution after treatment was favorable. Complete surgical resection of the tumor is usually sufficient, but there are reported cases with recurrence.
ABSTRACT
Burkitt's lymphoma can show in a variety of ways, and it's frequently identified in children owing to the development of an abdominal tumor. This aggressive, fast growing tumor can induce either indirect symptoms due to pressure phenomena or direct involvement of the intestine lumen, resulting in intestinal obstruction or intussusception. We are reporting a case of intestinal intussusception in a patient with Burkitt's lymphoma.