Subject(s)
Behcet Syndrome/diagnosis , Polyradiculoneuropathy/diagnosis , Acute Disease , Adolescent , Behcet Syndrome/complications , Behcet Syndrome/pathology , Diagnosis, Differential , Humans , Male , Polyradiculoneuropathy/etiology , Polyradiculoneuropathy/pathology , Scrotum/pathology , Skin Ulcer/diagnosis , Skin Ulcer/pathology , Stomatitis, Aphthous/diagnosis , Stomatitis, Aphthous/etiology , Stomatitis, Aphthous/pathologyABSTRACT
Dermatomyositis is a rare connective tissue disease of unknown origin, including inflammatory myopathy and cutaneous manifestations. Several pulmonary complications associated to dermatomyositis were described; especially interstitial lung disease. Some rare and particular pulmonary complications were reported in the literature such as pneumodiastinum and pneumothorax. We are describing here, a case report about a female patient, who presented with dermatomyositis associated to pneumomediastinum as a severe and lethal complication without pneumothorax. It is a novel observation depicting this severe and rare complication. Brutal dyspnea and cervical subcutaneous crackling are alarming signs that should make practitioners think about this complication.