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Rev Pneumol Clin ; 73(5): 258-262, 2017 Oct.
Article in French | MEDLINE | ID: mdl-29054712

ABSTRACT

Dermatomyositis is a rare connective tissue disease of unknown origin, including inflammatory myopathy and cutaneous manifestations. Several pulmonary complications associated to dermatomyositis were described; especially interstitial lung disease. Some rare and particular pulmonary complications were reported in the literature such as pneumodiastinum and pneumothorax. We are describing here, a case report about a female patient, who presented with dermatomyositis associated to pneumomediastinum as a severe and lethal complication without pneumothorax. It is a novel observation depicting this severe and rare complication. Brutal dyspnea and cervical subcutaneous crackling are alarming signs that should make practitioners think about this complication.


Subject(s)
Dermatomyositis/complications , Mediastinal Emphysema/etiology , Dermatomyositis/pathology , Female , Humans , Mediastinal Emphysema/pathology , Middle Aged , Subcutaneous Emphysema/etiology , Subcutaneous Emphysema/pathology
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