ABSTRACT
We report on an infant in whom bilateral renal cysts were the only initial manifestation of tuberous sclerosis. We review the reported cases of infants with this association and emphasize that tuberous sclerosis can present in infancy as bilateral renal cystic disease. The role of the kidney biopsy in providing the correct diagnosis is discussed.
Subject(s)
Kidney Diseases, Cystic/complications , Tuberous Sclerosis/diagnosis , Female , Humans , Infant , Kidney Diseases, Cystic/diagnosis , Kidney Diseases, Cystic/pathology , Tuberous Sclerosis/complicationsABSTRACT
Continent urinary diversion (Florida Pouch) has been performed on 151 patients. The surgical technique utilizes a detubularized extended right colon segment, a doubly-plicated segment of ileum and a non-tunneled uretero-intestinal anastomosis. Mortality rate was 1.3%. Early and late complication rates have been minimal. 2.8% were incontinent. No radiographic renal damage has been noted and electrolyte abnormalities have not been a problem. The procedure is highly recommended to those surgeons performing continent urinary diversions.
