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Repert. med. cir ; 24(2): 152-156, 2015. tab
Article in English, Spanish | LILACS, COLNAL | ID: lil-795713

ABSTRACT

El feocromocitoma es una neoplasia neuroendocrina de células cromafines que biosintetiza, almacena, metaboliza y secreta concentraciones elevadas de catecolaminas y sus metabolitos. La incidencia es de dos a ocho casos por millón y es frecuente en la cuarta y quinta décadas de la vida. Presentación del caso: mujer de 19 años con cifras tensionales elevadas en controles médicos por antecedente de asma desde la niñez, que se estudia con análisis bioquímicos y TAC abdominal. Se llevó a cirugía ante la sospecha de un tumor adrenal y la neoplasia se caracteriza en el servicio de patología. Conclusiones: el diagnóstico de feocromocitoma y paragangliomas simpáticos que sintetizan y secretan catecolaminas (adrenalina, noradrenalina y dopamina) se basa en el examen físico y el estudio analítico; el principal síntoma es hipertensión arterial. El tratamiento es quirúrgico con curación completa en más del 90%...


Pheochromocytomas are neuroendocrine cromaffin cell tumors which synthetize store, and secrete high concentrations of catecholamines and their metabolytes. Incidence is two to eight cases per million and they are most common in the fourth and fifth decades of life. Case report: a 19-year-old woman with high blood pressure levels in medical follow-ups for presenting asthma since her childhood. She is studied by biochemical analyses and abdominal CT scan. She undergoes surgery due to suspicion of an adrenal tumor and the surgical specimen is characterized in the pathology service. Conclusions: the diagnosis of pheochromocytoma and simpathetic paragangliomas which synthetize and secrete catecholamines (adrenaline, noradrenaline and dopamine) is based on physical exam and complete analyses; the main symptom is arterial hypertension. Surgery is the basis of therapy with complete healing in more than 90% of cases...


Subject(s)
Humans , Female , Young Adult , Pheochromocytoma , Adrenal Glands , Hypertension , Paraganglioma
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