ABSTRACT
Extrapontine myelinolysis in the pediatric age group is very rare. We report a nine-year-old girl with the classical clinical syndrome of pontine and extrapontine myelinolysis following liver trauma due to a traffic accident. She was referred to our hospital for further investigation of convulsions due to severe postoperative hyponatremia. She had no hypoxic event or other identifiable cause for the neurological symptoms. Neurological deterioration began about two days after correction of hyponatremia and followed a period of temporary improvement in hyponatremic encephalopathy. Diagnosis of extrapontine myelinolysis was confirmed with the identification of typical features on magnetic resonance imaging. The rapid correction of hyponatremia seemed the most likely cause since other biochemical tests including liver function tests were all within normal ranges. The long term clinical outcome was good. It is important to carefully monitor the rate of correction in electrolyte disturbances, and to consider the individual variation in response to therapy.
Subject(s)
Demyelinating Diseases/diagnosis , Demyelinating Diseases/etiology , Hyponatremia/complications , Accidents, Traffic , Child , Female , Fluid Therapy/adverse effects , Humans , Hyponatremia/therapy , Liver/injuries , Magnetic Resonance Imaging , Seizures/etiologyABSTRACT
A case of an ectopic scrotum located in the right inguinal area is described. The left hemiscrotum was in normal location, and each hemiscrotum contained testis. The boy also had an infralevator-type anorectal malformation. Initially, anoplasty was performed, and scrotal reconstruction was carried out 1 month later. The authors also reviewed the embryological explanation of ectopic scrotum in the literature.
Subject(s)
Abnormalities, Multiple/surgery , Anus, Imperforate/surgery , Choristoma/congenital , Choristoma/surgery , Groin , Scrotum , Abnormalities, Multiple/embryology , Anus, Imperforate/embryology , Choristoma/embryology , Humans , Infant, Newborn , Male , Scrotum/embryologyABSTRACT
Intestinal atresia is the most frequently encountered cause of ileus in the neonate. Of all atresias combination of small and large bowel atresias is extremely rare. In 1973, Guttman presented a case with multiple, widespread atresias of small and large bowel, intraluminal calcifications and a hereditary nature. This paper describes the detailed pathological findings of a similar case of multiple intestinal atresias and discusses for the pathogenesis of this rare condition.
Subject(s)
Infant, Premature, Diseases/diagnosis , Intestinal Atresia/diagnosis , Fatal Outcome , Humans , Infant, Newborn , Infant, Premature, Diseases/pathology , Intestinal Atresia/genetics , Intestinal Atresia/pathology , Intestines/pathology , MaleABSTRACT
Juvenile xanthogranuloma (JX) is a regressing fibrous histiocytoma occurring during infancy and characterized by cutaneous papules and nodules and less often by additional lesions in deep tissue and organs. It has a special place among childhood masses by presenting different outcomes and spontaneous regression. We report three cases of JX that were detected after birth and resected.
