ABSTRACT
OBJECTIVE: To describe a case of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome associated with bilateral myomas in uterine remnants. DESIGN: Case report. SETTING: University hospital. PATIENT(S): A 35-year-old woman with MRKH syndrome and pelvic pain, in whom leiomyomas were diagnosed by imaging techniques. INTERVENTION(S): Diagnostic laparoscopy followed by excision of leiomyomas and uterine remnants by laparotomy. MAIN OUTCOME MEASURE(S): Resolution of symptoms and histologic confirmation of the clinic diagnosis. RESULT(S): After a 6-month follow-up period, the patient was asymptomatic. The histologic examination confirmed MRKH syndrome associated with multiple myomas in both rudimentary uteri. CONCLUSION(S): This is an unusual case of MRKH syndrome associated with bilateral leiomyomas. The excision of the tumors with the adjacent uterine remnants is indicated when they are symptomatic.
