[Case of Gorlin syndrome]. / A propósito de un caso de "sindrome de Gorlin".

In this paper we report a Gorlin's syndrome in a patient, who was first diagnosed as a case of a large odontogenic keratocyst. Posterior analysis demonstrate the presence of other keratocyst in the maxilla and in the mandible, as well as lumbar scoliosis, lack and malformation of ribs, calcification of the brain sickle and folicles of 8 mm of diameter in the right ovary. The possible presence of nevoid basal cell carcinomas will be also considered.