ABSTRACT
El nevo lipomatoso cutáneo superficial es una entidad rara, de carácter hamartomatoso caracterizada por la presencia de tejido adiposo maduro ectópico en la dermis superficial, que aparece en las tres primeras décadas de la vida. Presentamos cuatro nuevos casos incluyendo un paciente con la más extensa afectación reportada hasta la fecha, la cual se asoció a lipomas masivos en el tejido celular subcutáneo y lipomatosis difusa. Hasta donde conocemos, este es el primer reporte sobre esta entidad realizado en Cuba (AU)
Nevus lipomatosus cutaneus superficialis is a rare, hamartomatous disorder, characterized by the presence of ectopic mature adipose tissue within the superficial dermis. Lesions occur within the first three decades of life. We report four new cases, including a patient with the most extensive affectation reported to date, which was associated with massive lipomas in the subcutaneous cell tissue and diffuse lipomatosis. To our knowledge, it is the first report of this disorder in Cuba (AU)
Subject(s)
Humans , Nevus/pathology , Lipoma/pathology , Skin Neoplasms/pathology , Hamartoma/pathology , Lipomatosis/complications , Adipose Tissue/pathology , Diagnosis, DifferentialABSTRACT
Nevus lipomatosus cutaneus superficialis is a rare, hamartomatous disorder, characterized by the presence of ectopic mature adipose tissue within the superficial dermis. Lesions occur within the first three decades of life. We report four new cases, including a patient with the most extensive affectation reported to date, which was associated with massive lipomas in the subcutaneous cell tissue and diffuse lipomatosis. To our knowledge, it is the first report of this disorder in Cuba.
Subject(s)
Lipoma/pathology , Lipomatosis/pathology , Neoplasms, Multiple Primary/pathology , Nevus/pathology , Skin Diseases/pathology , Skin Neoplasms/pathology , Adult , Humans , Lipoma/complications , Lipomatosis/complications , Male , Middle Aged , Neoplasms, Multiple Primary/complications , Nevus/complications , Skin Diseases/complications , Skin Neoplasms/complicationsABSTRACT
La Lipomatosis Múltiple Simétrica (LMS), también conocida como síndrome de Launois-Bensaude, constituye una condición de origen desconocido caracterizada por un depósito simétrico de tejido adiposo en cuello, tronco, cabeza y extremidades superiores, reportándose hasta el momento poco más de 200 casos en la literatura. Realizamos la presentación de un paciente con esta rara afección, así cómo una revisión del estado actual de esta enfermedad(AU)
Multiple symmetric lipomatosis, also known as Launois- Bensaude syndrome, constitute an unknown condition characterized by a symmetric deposits of fat beneath the skin of the neck, trunk, head and upper extremities, reporting more than 200 cases in literature nowadays. It is presented a case of a patient with this weird disease, as well as a revision of a current stage of this condition(EU)
