1.
Arch Pediatr
; 20(4): 369-71, 2013 Apr.
Article
in French
| MEDLINE
| ID: mdl-23433844
ABSTRACT
Erythromelalgia is a rare disease whose etiology is poorly understood. It is characterized by paroxysmal attacks of erythema, pain, and warmth of the extremities and can be primary or secondary. We report a case of primary familial erythromelalgia and stress the difficulties in its therapeutic management. We provide a brief update on the pathophysiology and treatment of primary erythromelalgia.