ABSTRACT
We report an unusual presentation of a case of Axenfeld-Rieger (A-R) syndrome. A 14-year-old male presented with gradual dimness of vision for 1 year and redness of left eye for 3 days. The patient had megalocornea with Haab's striae in the right eye and posterior embryotoxon in both the eyes. In the left eye, there was a white cord-like structure traversing the anterior chamber with adhesions to iris tissue along its course. On two antiglaucoma medications, his intraocular pressure (IOP) was 22 mm Hg in the right eye and 18 mm Hg in the left eye. Gonioscopy revealed a cord-like structure originating at the level of Schwalbe's line. He underwent right eye trabeculectomy with mitomycin-C. This case highlights a rare presentation of a strange cord-like structure, a rare presentation of A-R syndrome.
Subject(s)
Anterior Chamber/pathology , Cornea/abnormalities , Eye Abnormalities/pathology , Adolescent , Anterior Eye Segment/abnormalities , Anterior Eye Segment/pathology , Anterior Eye Segment/physiopathology , Anterior Eye Segment/surgery , Eye Abnormalities/complications , Eye Abnormalities/physiopathology , Eye Abnormalities/surgery , Eye Diseases, Hereditary , Gonioscopy , Humans , Intraocular Pressure , Iris/pathology , Male , Mitomycin/therapeutic use , Tissue Adhesions/pathology , Trabeculectomy , Vision Disorders/etiologyABSTRACT
The sulphonamide group of drugs is implicated in bilateral acute angle closure (AAC) due to an idiosyncratic response. We report a series of three cases with bilateral AAC caused by different sulphonamide derivatives, their presentation and management.
