1.
Bull Cancer
; 80(9): 816-9, 1993 Sep.
Article
in French
| MEDLINE
| ID: mdl-8204959
ABSTRACT
Maffucci's syndrome was first described in 1881 and results of a mesodermic dysembryoplasia, congenital but not hereditary. Pathogenic hypothesis are multiple. This syndrome is characterized by the occurrence of multiple haemangiomas in the soft tissue, and multiple enchondromas of the bones. The association of ovary tumor is however exceptional. Four cases are reported in the literature; we report the fifth case.