ABSTRACT
PURPOSE: Spinal angiolipomas are benign spinal epidural tumors consisting of mature fat cells with angiomatous components. These tumors are rare in children and there are no definite management guidelines. METHOD: To the best of our knowledge, only five cases of spinal angiolipomas have been reported in children below 12 years. This article discusses the presentation, diagnostics, and surgical tips for the management of a case of spinal angiolipoma. RESULT: In this paper, we present a one and half-year-old child presenting with a spontaneous spinal epidural hematoma from a spinal angiolipoma and underscore the importance of early surgery in a benign disease for a good outcome. CONCLUSION: Overall neurological recovery and prognosis following timely intervention for spinal angiolipomas are good.
Subject(s)
Angiolipoma , Hematoma, Epidural, Spinal , Spinal Neoplasms , Angiolipoma/complications , Angiolipoma/diagnostic imaging , Angiolipoma/surgery , Epidural Space , Humans , Infant , Magnetic Resonance Imaging , Paraplegia/etiology , Spinal Neoplasms/complications , Spinal Neoplasms/diagnostic imaging , Spinal Neoplasms/surgerySubject(s)
Craniotomy/adverse effects , Dust , Edema/surgery , Epilepsy/surgery , Malformations of Cortical Development, Group I/surgery , Postoperative Complications/surgery , Seizures/surgery , Skull , Adult , Edema/etiology , Epilepsy/complications , Humans , Male , Malformations of Cortical Development, Group I/complications , Postoperative Complications/etiology , Seizures/etiology , Treatment OutcomeABSTRACT
BACKGROUND: A persistent craniopharyngeal canal (PCC) is a rare cause of cerebrospinal fluid rhinorrhea in children. The condition often coexists with other midline facial defects, such as cleft palate. Children with PCC may also have pituitary dysfunction or neoplasms, such as craniopharyngiomas within the canal. CASE DESCRIPTION: A 5-year-old girl presented with bacterial meningitis and active cerebrospinal fluid rhinorrhea from her left nostril. Imaging showed a large nasopharyngeal meningoencephalocele, communicating with the subarachnoid space through a persistent craniopharyngeal canal. An endonasal approach was chosen to excise the PCC and meningoencephalocele and to repair the resulting skull base defect. CONCLUSIONS: The extended endonasal approach can be used to treat PCC with nasopharyngeal encephaloceles in young children. The approach is suitable to address both conditions at the same time. The extended endonasal approach avoids potentially morbid transfacial approaches and can help in earlier recovery after surgery.