ABSTRACT
Hemangioendothelioma is a vascular tumor of endothelial cell origin. It may involve bone or soft tissues and can behave like a benign or malignant tumor. In the literature, there are several case reports on the involvement of the head and neck region, but involvement of the frontal bone is extremely rare. This report presents the case of a 4-year-old boy with the diagnosis of spindle cell hemangioendothelioma of the frontal bone, who was treated by wide surgical resection.
Subject(s)
Frontal Bone/pathology , Hemangioendothelioma/pathology , Skull Neoplasms/pathology , Child, Preschool , Craniotomy/methods , Frontal Bone/surgery , Hemangioendothelioma/surgery , Humans , Male , Skull Neoplasms/surgeryABSTRACT
Vascular tumors are rarely encountered in the paranasal sinuses. When they do arise there, they can be life-threatening because of the risk of bleeding. Embolization alone and in combination with surgical resection has been the mainstay of treatment. We report the case of a prepubertal girl who experienced two recurrences of arteriovenous malformation, one in the maxillary sinus and the other in the mandible. To our knowledge, this is the first report in the literature of recurrences arising in these two locations.
Subject(s)
Hemangioma/surgery , Mandibular Neoplasms/surgery , Maxillary Sinus Neoplasms/surgery , Neoplasm Recurrence, Local/surgery , Child , Embolization, Therapeutic , Female , Hemangioma/diagnosis , Humans , Mandibular Neoplasms/diagnosis , Maxillary Sinus Neoplasms/diagnosisABSTRACT
OBJECTIVES: We evaluated the results of orbital decompression in patients with Graves' disease. PATIENTS AND METHODS: Orbital decompression was performed by endoscopic transnasal medial wall approach and transantral inferior wall approach in 18 eyes of 12 patients (8 males, 4 females; mean age 41 years; range 24 to 65 years). The degree of exophthalmos was evaluated with the use of the Hertel exophthalmometer preoperatively, and postoperatively in the 24th hour, first and third months. RESULTS: At the end of the third month, exophthalmos decreased by a mean of 4.4 mm (range 3 to 7 mm). Visual acuity and field defects improved considerably in all patients. Complications occurred in three cases (25%) including diplopia, displacement of one eye inferiorly, and maxillary sinusitis caused by the encroachment of the adipose tissue upon the ostium, respectively. CONCLUSION: With the increasing ease of surgical procedures and enhanced experience on the part of surgeons, successful treatment of exophthalmos has become possible with decreased complication rates.
Subject(s)
Decompression, Surgical , Graves Disease/surgery , Orbit/surgery , Adolescent , Adult , Decompression, Surgical/methods , Endoscopy/methods , Female , Graves Disease/complications , Graves Disease/diagnostic imaging , Humans , Male , Middle Aged , Nasal Cavity/surgery , Postoperative Complications , Tomography, X-Ray Computed , Treatment Outcome , Visual AcuityABSTRACT
Lipoid proteinosis is a rare disease that presents with hyaline deposits in many tissues. It involves predominantly the skin and upper aerodigestive tract, presenting with small yellowish papules and hoarseness. It may involve the central nervous system and cause intracerebral calcifications. Laryngeal lesions may resemble singer's nodule or chronic laryngitis. The pathogenesis of the disease is not clear although several studies suggest a defective collagen production and/or lysosomal storage disease. In this article two cases with skin and larynx involvement are reported.
