1.
Rev Esp Enferm Dig
; 88(1): 43-5, 1996 Jan.
Article
in Spanish
| MEDLINE
| ID: mdl-8616001
ABSTRACT
Ehlers-Danlos syndrome type IV is a heritable disease of type III collagen metabolism. Most patients have a defect either in the synthesis or structure of type III procollagen, a finding consistent with the fact that these patients are prone to spontaneous rupture of the aorta and intestines, tissues rich in type III collagen. The diagnosis is suspected in a patient with a combination of clinical manifestations and family history, but it is confirmed only by culture of the patient's skin fibroblasts and the demonstration of a defect in type III collagen metabolism. We present a patient with Ehlers-Danlos type IV syndrome who developed a recurrent colon perforation, and discuss the surgical strategy to prevent recurrences.
Subject(s)
Ehlers-Danlos Syndrome/complications , Intestinal Perforation/etiology , Sigmoid Diseases/etiology , Adult , Colon, Sigmoid/pathology , Ehlers-Danlos Syndrome/pathology , Female , Humans , Intestinal Perforation/pathology , Intestinal Perforation/surgery , Recurrence , Sigmoid Diseases/pathology , Sigmoid Diseases/surgery
2.
Rev Esp Enferm Apar Dig
; 71(4): 299-304, 1987 Apr.
Article
in Spanish
| MEDLINE
| ID: mdl-3602563
Subject(s)
Liver Abscess , Adult , Aged , Aged, 80 and over , Drainage , Female , Humans , Liver Abscess/complications , Liver Abscess/etiology , Liver Abscess/surgery , Male , Middle Aged , Prognosis
3.
Rev Esp Enferm Apar Dig
; 65(2): 171-6, 1984 Feb.
Article
in Spanish
| MEDLINE
| ID: mdl-6739937
4.
Rev Esp Enferm Apar Dig
; 44(6): 563-74, 1974 Nov 15.
Article
in Spanish
| MEDLINE
| ID: mdl-4438785
Subject(s)
Cholelithiasis/pathology , Liver/pathology , Adult , Aged , Biopsy , Cholangiography , Cholecystectomy , Cholelithiasis/enzymology , Diagnosis, Differential , Female , Flocculation Tests , Humans , Liver/enzymology , Male , Middle Aged
5.
Rev Esp Enferm Apar Dig
; 44(4): 387-400, 1974 Oct 15.
Article
in Spanish
| MEDLINE
| ID: mdl-4438773
Subject(s)
Tuberculosis, Hepatic , Aged , Diagnosis, Differential , Humans , Liver/pathology , Male , Tuberculosis, Hepatic/pathology
6.
Rev Esp Enferm Apar Dig
; 43(2): 165-76, 1974 Mar 15.
Article
in Spanish
| MEDLINE
| ID: mdl-4840485