ABSTRACT
Chiari malformation is characterized by caudal displacement of the cerebellar tonsils that penetrate into the spinal canal through the foramen magnum, achieving reach the atlas or axis. trunk and any drop of the fourth ventricle is observed. Typically is seen in young adults. In some cases scoliosis and Syringomyelic cavities may occur. The authors present (as far as they know) the first case in the literature with long term follow-up, of a caucasian woman with an unusual form of cerebellar atrophy and Chiari Type I malformation, suffering from weakness in his upper and lower extremities with rapidly progression. The patient was successfully treated with suboccipital decompression and C1 laminectomy.
La malformación de Chiari se caracteriza por un desplazamiento caudal de las amígdalas cerebelosas que penetran hacia el canal raquídeo por el foramen mágnum, logrando llegar hasta el atlas o el axis. No hay descenso del tronco y tampoco del cuarto ventrículo. Típicamente se observa en adultos jóvenes. En algunos casos hay escoliosis y cavidades siringomiélicas. Los autores presentan lo que a su conocimiento es el primer caso de la literatura con seguimiento a largo plazo de una mujer de raza blanca con una forma inusual de atrofia cerebelosa y malformación de Chiari tipo I, que sufre de debilidad en sus extremidades superiores e inferiores rápida y progresivamente. La paciente fue tratada con éxito mediante descompresión suboccipital y laminectomia C1.
Subject(s)
Arnold-Chiari Malformation/diagnosis , Arnold-Chiari Malformation/pathology , Cerebellum/pathology , Adolescent , Arnold-Chiari Malformation/complications , Atrophy/etiology , Female , HumansABSTRACT
Introducción y objetivos Las fístulas arteriovenosas piales son malformaciones vasculares infrecuentes. Generalmente son congénitas y su historia natural es ominosa. El objetivo es describir nuestra experiencia en su manejo endovascular y analizar la literatura. Pacientes y métodos Es un estudio retrospectivo descriptivo de pacientes tratados por vía endovascular durante 3 años en 3 instituciones latinoamericanas. Resultados Fueron 6 pacientes con edad media de 22 años. Un caso fue resultado de un traumatismo. El 50% presentó hemorragia intracraneal, el 66% desarrollaron clínica secundaria a efecto de masa y al flujo retrógrado. En los estudios de imagen se observaron varices intracraneales en el 83% de los casos. La angiografía cerebral mostró arterias fistulosas provenientes de la circulación anterior en el (..) (AU)
Subject(s)
Humans , Arteriovenous Fistula/surgery , Endovascular Procedures/methods , Vascular Malformations/surgery , Retrospective Studies , NeuroimagingABSTRACT
INTRODUCTION AND OBJECTIVES: Pial arteriovenous fistulas are infrequent vascular malformations. They are generally congenital and their natural history is ominous. The objective of this work is to describe our experience in their endovascular management and to review the existing literature. PATIENTS AND METHODS: This is a retrospective and descriptive study of patients treated by endovascular approach during 3 years at 3 Latin-American hospitals. RESULTS: The study included 6 patients with a mean age of 22 years. One case was caused by cranial trauma. In total, 50% suffered intracranial haemorrhage and 66% developed symptoms attributable to volume effect or retrograde blood flow. Intracranial varices were identified by CT and MRI scans in 83% of cases. Digital subtraction angiography showed arteriovenous fistulas from anterior circulation in 67% of cases and deep venous drainage in 50%. One endovascular procedure was performed in 5 cases (83%), while 2 procedures were required in one case. A single embolic agent was used to occlude fistulas in 67% of cases; whilst 33% required a combination. Coils were used in 4 cases (67%) and onyx was injected in another 4 (67%). One case required stent and balloon deployment. The fistulas were uneventfully occluded in all cases. The follow-up period was one year in 5 cases and 6 months in one case. All patients remained symptom-free. CONCLUSIONS: Endovascular management can be considered as the treatment of choice. It consists in the embolisation of arterial pedicles with one or more embolic agents and should be performed as close as possible to the drainage vein, avoiding migration of the embolic agent towards the venous side.
Subject(s)
Polyvinyls , Treatment Outcome , Arteriovenous Fistula , Embolization, Therapeutic , Humans , Retrospective StudiesABSTRACT
Carotid atherosclerosis accounts for about 25 % of all ischemic cerebrovascular events. A thorough knowledge of the pathophysiology of the plaque and its clinical consequences are fundamental elements for a well-balanced approach of the management of the disease. The evolution of the imaging techniques allow to visualize the plaque and the analysis of its structure and characteristics. The awareness of the physiopathology and the understanding of the imaging modalities are key issues when planning the treatment of the patient.
Subject(s)
Atherectomy , Carotid Artery Diseases/diagnosis , Carotid Artery Diseases/surgery , Stents , HumansABSTRACT
Carotid endarterectomy has for long been regarded as the gold standard for the management of symptomatic atherosclerosis of the carotid bifurcation, and carotid angioplasty is merely considered a secondary alternative reserved to surgically high-risk patients. However, several studies have shown that the efficacy of carotid angioplasty has equaled that of carotid endarerectomy and additionally provides unshared advantages: local anesthesia is sufficient, the whole extracranial and intracranial carotid circulation are amenable to treatment and wound-related complications are not seen. Besides a thorough review of the main published studies comparing both techniques, we provide updated criteria for the endovascular management of carotid artery disease, discussing their benefits and limitations.
