ABSTRACT
Acquired melanocytic lesions resembling malignant melanoma have been described in all major categories of Epidermolysis bullosa and referred to as "Epidermolysis bullosa nevi''. They easily induce to diagnostic error, although no malignant transformation has been reported. We report the development of a large acquired melanocytic nevus at a site of recurrent blisters in a 5-year-old child with Epidermolysis bullosa simplex. The global dermoscopic pattern was suggestive of benignity, and the histopathological findings were compatible with a compound melanocytic nevus. This is the first published case of Epidermolysis bullosa nevi in Brazilian literature. Despite their benign behavior, we emphasize the importance of regular clinical and dermoscopic monitoring, since a malignant course still cannot be totally excluded.
Subject(s)
Epidermolysis Bullosa Simplex/complications , Nevus, Pigmented/complications , Skin Neoplasms/complications , Child, Preschool , Female , Humans , Nevus, Pigmented/diagnosis , Skin Neoplasms/diagnosisABSTRACT
Lesões melanocíticas adquiridas assemelhando-se à melanoma têm sido descritas nos principais grupos da Epidermólise bolhosa, e referidas como "Nevos da Epidermólise bolhosa''. Induzem facilmente ao erro diagnóstico, apesar de nenhuma transformação maligna ter sido descrita. Relatamos o desenvolvimento de um nevo melanocítico adquirido grande no local de bolhas recorrentes em uma criança de 5 anos portadora de Epidermólise bolhosa simples. O padrão dermatoscópico global foi sugestivo de benignidade, e os achados histopatológicos foram compatíveis com um nevo melanocítico composto. Este é o primeiro caso de um Nevo da Epidermólise bolhosa publicado na literatura brasileira.
Acquired melanocytic lesions resembling malignant melanoma have been described in all major categories of Epidermolysis bullosa and referred to as "Epidermolysis bullosa nevi''. They easily induce to diagnostic error, although no malignant transformation has been reported. We report the development of a large acquired melanocytic nevus at a site of recurrent blisters in a 5-year-old child with Epidermolysis bullosa simplex. The global dermoscopic pattern was suggestive of benignity, and the histopathological findings were compatible with a compound melanocytic nevus. This is the first published case of Epidermolysis bullosa nevi in Brazilian literature. Despite their benign behavior, we emphasize the importance of regular clinical and dermoscopic monitoring, since a malignant course still cannot be totally excluded.
Subject(s)
Child, Preschool , Female , Humans , Epidermolysis Bullosa Simplex/complications , Nevus, Pigmented/complications , Skin Neoplasms/complications , Nevus, Pigmented/diagnosis , Skin Neoplasms/diagnosisABSTRACT
Congenital erosive and vesicular dermatosis healing with reticulated supple scarring is a rare disease first reported by Cohen et al in 1985. To date only 13 cases of this disease have been reported. This entity is characterized by the presence of erosions and vesicles at birth, usually affecting about 75% of the body which heals with reticulated scarring in weeks to months. We report a case of this disease related to a boy who was born with erosions affecting his head, trunk, and limbs. All lesions healed completely after 3 months with reticulated scarring without any clinical complications.
Subject(s)
Cicatrix/etiology , Skin Diseases, Vesiculobullous/congenital , Skin Diseases, Vesiculobullous/pathology , Cicatrix/pathology , Humans , Infant, Newborn , Male , Skin Diseases, Vesiculobullous/complicationsSubject(s)
Scalp Dermatoses , Skin Diseases , Dermatology , Facial Dermatoses , Leg Dermatoses , Hand Dermatoses , Foot Dermatoses , Wounds and InjuriesABSTRACT
Os autores apresentam três casos de piedra branca comprometendo o couro cabeludo de crianças em idade pré-escolar. O Trichosporon beigelii foi caracterizado por exames micológicos. Revisa-se a literatura abordando aspectos clínicos, micológicos e terapêuticos
Subject(s)
Humans , Female , Child, Preschool , Child , Piedra/microbiology , Scalp/microbiology , Mercuric Chloride/therapeutic use , Piedra/drug therapy , Piedra/pathology , Trichosporon/isolation & purificationABSTRACT
Realizou-se uma revisäo da Progeria, Pangeria, Metageria e Acrogeria, síndromes genéticas que de forma prematura imitam clinicamente as modificaçöes do envelhcimento cronológico ou normal. Foram analisadas as manifestaçöes clínicas, dermatológicas, histopatológicas e bioquímicas e discutidas suas semelhanças e diferenças como o envelhecimento cronológico
