ABSTRACT
Focal fibrocartilaginous dysplasia is an uncommon benign bone condition that predominantly affects children and typically leads to varus deformities in the proximal tibia. It was first described by Bell in 1985. The etiology remains unknown and the diagnosis is radiological; biopsy is not necessary. We present a case of a 2-year-old child who presented to our department for a right limb varus deformity caused by focal fibrocartilaginous dysplasia.
ABSTRACT
Osteosarcoma (OS) is the most common primary non hematopoietic malignant tumor of bone with a strict histologic definition: the presence of unequivocal osteoid produced by neoplastic cells. Rare variants displaying low-grade histological features have been described; among which chondromyxoid fibroma-like (CMF-OS) is the rarest. However, despite its bland morphology; CMF-like OS has an aggressive clinical behavior and a poor prognosis. To the best of our knowledge, only 3 cases of CMF-OS have been previously reported in children. Because of its atypicality and scarcity; misdiagnosis is more likely to occur. Herein we describe a new case of CMF-OS in a 13 years old girl with fatal outcome. Diagnosis was based on focal malignant bone formation and correlation with imaging studies. The aim of the present case presentation is to raise awareness of this rare entity and to highlight the challenging diagnosis.
ABSTRACT
Anevrysmal bone cyst is an aggressive, destructive but benign lesion in the long bones, spine or basin, affecting mainly children and young adults. However, it is a very rare tumor. We here report the case of a 8-year old boy with a very rare localization of anevrysmal cyst in the clavicle, initially presenting with pathologic bone fracture, that is a benign cystic lesion. The child underwent complete radical resection of the cyst located at the level of the right clavicle, followed by anatomopathological examination of surgical specimen which confirmed the diagnosis. Patient's evolution was marked by the absence of recurrences and by good radiologic bone remodeling. Radical cyst resection seems to avoid recidivism. This study aims to update the current understanding of this rare orthopaedic condition by comparing our results with those reported in the world literature.
Subject(s)
Bone Cysts, Aneurysmal/pathology , Bone Remodeling , Clavicle/pathology , Bone Cysts, Aneurysmal/diagnosis , Bone Cysts, Aneurysmal/surgery , Child , Clavicle/surgery , Fractures, Bone/diagnosis , Humans , MaleABSTRACT
Tuberculosis of bone is an infectious disease which represents a major public health problem in developing countries where it is endemic. Osteoarticular involvement accounts for 1-5% of all cases of tuberculosis, shoulder involvement is very rare and accounts for 1-2% of all cases of osteoarticular tuberculosis. We here report an uncommon case of TB infection involving the scapula, reaching the scapular body. Tuberculosis is still an important differential diagnosis of rare or chronic bone diseases, including tumors. In our study anatomopathological examination led to the diagnosis.
Subject(s)
Scapula/pathology , Tuberculosis, Osteoarticular/diagnosis , Child , Diagnosis, Differential , Humans , Male , Tuberculosis, Osteoarticular/pathologyABSTRACT
INTRODUCTION: We retrospectively reviewed 106 pediatric cases of peripheral osteoarticular tuberculosis (OAT) seen over a 21-year period in Morocco. Patients with vertebral tuberculosis were excluded from the study. PATIENTS AND RESULTS: The 55 boys and 51 girls had a mean age of 8 years. The hip and knee together contributed 63% of the osteoarticular foci. Organ involvement was documented in 32 cases. Mean time from symptom onset to evaluation was 10 months. This resulted in diagnostic delay, which contributed to the 22% rate of residual abnormalities consisting of joint ankylosis and leg length inequality. CONCLUSION: OAT is a source of functional disability that should be recognized and treated early, particularly in children, given that appropriate management can lead to a full recovery (14 patients in our series).
