ABSTRACT
We present an uncommon case of a pediatric patient with sudden-onset sensorineural hearing loss (SSNHL), a medical condition in which a person experiences a rapid loss of 30 or more decibels within a matter of hours or days. The patient is a nine-year-old female who, two years prior, suddenly lost hearing in her left ear after a 24-hour episode of nausea, vomiting, and left ear pain. She presented to our clinic two years after the episode, long after the window for evidence-based treatment for acute SSNHL, such as corticosteroid therapy or antivirals, had passed. However, she remembered the moment of her hearing loss vividly, an uncommon occurrence in pediatric patients. CT, MRI, family history, and physical exam were unremarkable. The patient had a brief hearing aid trial where she described being able to hear the sound but did not have any clarity in understanding the sound. The patient was ultimately treated with a unilateral cochlear implant and showed excellent subjective and audiogram responses. Continued research on the management of SSNHL in pediatric patients who present outside of the acute therapeutic window is needed.
ABSTRACT
We discuss the unusual presentation and subsequent diagnosis of a patient with a glomus tympanicum tumor, also known as middle ear paraganglioma, which is a rare and benign tumor of the middle ear that usually presents with pulsatile tinnitus, cranial nerve pathology, hearing loss, and dizziness. The patient was a 35-year-old female with no past medical or surgical history who presented with a three-year history of mild left-ear hearing loss. The initial examination was negative for otalgia or otorrhea but was notable for a mass filling her left ear canal. The patient denied pulsatile tinnitus or dizziness. CT imaging was used to examine the soft tissue mass in the middle ear and ear canal and was consistent with a soft tissue heterogeneous mass with a subsequent biopsy confirming a diagnosis of paraganglioma. After the diagnosis, a laser surgical excision was scheduled to remove the tumor. Constant awareness is needed to examine the different presentations of middle ear paragangliomas so that appropriate treatment is promptly provided.
