Hyperglycaemia and ß-cell antibodies: is it always pre-type 1 diabetes?

We describe 10-year-old girl with mild incidental hyperglycaemia, impaired glucose tolerance and GADA positivity. Family history for mild hyperglycaemia and GADA fluctuation alerted us to a possible MODY diagnosis which was confirmed by detection of GCK mutation c.626C>T; p.T209M. Weak or transient ß-cell autoimmunity should not preclude genetic testing for MODY when the clinical features are suggestive.