[Currarino triad: different forms of presentation]. / Triada de Currarino: sus diferentes formas de presentación.

BACKGROUND: We describe our experience in Currarino syndrome (CS) and our clinical findings. METHODS: Case 1: Newborn female with prenatal diagnosis of myelomeningocele which was confirmed at birth as a lipomyelomeningocele, associated with partial sacral agenesis, horseshoe kidney and complex anorectal malformation with colonic vascular anomaly. Case 2: A 14-month-old male with constipation. The physical examination detected an anal stricture and radiological findings of a presacral lipomeningocele plus teratoma and a partial sacral agenesis. Case 3: An 8-month-old male with recurrent meningitis associated with anterior sacral meningocele and rectal fistula. An anal stricture and hemisacrum were also demonstrated. RESULTS: In case 1, an abdomino-perineal pull-through was performed but it failed because of her colonic vascular anomaly. Nowadays she is 3 years old and has a cecostomy, controls her micturition and is able to walk. Case 2 is two years old with satisfactory flow-up-after the teratoma and meningocele removal plus anal dilation. In case 3 a colostomy was necessary because after mass excision a recto-cutaneous fistula appeared during postoperative period. A ventriculoperitoneal valve implantation due to his hydrocephaly was also performed. CONCLUSIONS: The constipation is the most common symptom in the CS. Recurrent meningitis has a high mortality rate (56%) due to rectomeningeal fistula. The most common anorectal malformation is the anal stricture, and the more complex the malformation is, higher will the risk of incontinence be. The success of the management and follow-up is a multidisciplinary responsability.

[Pancreatic pseudocyst: less is more]. / Pseudoquiste pancreático: cuando menos es más.

UNLABELLED: Pancreatic pseudocysts (PQP) are rare in childhood and management tends to be individualized and controversial, and it is a challenge for the pediatric surgeon. The aim of this study is to determine the best management strategies in each patient. MATERIAL AND METHODS: Retrospective review of children admitted to our institution with the diagnosis of PQP and review of literature between 1990 and 2007. RESULTS: We report two children with postraumatic PQP that respond to non-operative management and 284 cases that were reported in literature (76% after blunt abdominal trauma). 26% of these patients had complete resolution of PQP with conservative management and the others patients required surgical intervention: external percutaneous drainage (18.6%), non-percutanueous external drainage drenaje (3.87%), cystogastrostomy (28.87%), cystojejunostomy o pancreaticojejunostomy (9.5%), endoscopic drainage (9.5%) or distal pancreatectomy (3.5%). CONCLUSION: The choice of treatment depends on the surgeon's experience and management of the endoscopic techniques, as well as the availability of interventionist radiology. Asymptomatic PQP in children does no require any specific intervention other than expectant management, especially in patients with trauma-induced PQP. Children with persistent clinical symptoms or those who developed complications may require further intervention.

[Must we change the surgical treatment of gallstones?]. / Hay que cambiar el planteamiento quirúrgico en las litiasis biliares?

UNLABELLED: The incidence of gallstones in childhood is 0.15%-0.22%. Frequency has increased in recent years due to a real increase or to a better diagnosis by ultrasound. The aim of our study is determinate the best treatment for every patient. MATERIALS AND METHODS: A retrospective study of 71 children with cholelithiasis admitted to our hospital in the last 20 years. RESULTS: The male to female ratio was 43:28. Seventeen patients present predisposing factors that might be related to the formation of gallstones. This disease was a casual event in half the cases. In 24 patients the diagnosis was made during a study for inspecific abdominal pain and 14 children showed typical symptoms. Only one patient suffer from acute cholecystitis. In 21 cases we find a single stone and in the other cases there were a lot of stones. The gallstones disappeared spontaneously in two patients. Nine children received treatment with ursodeoxycholic acid, but this treatment was ineffective in 8 of them. 27 patients were operated: Six laparoscopic cholecystectomy, 9 open cholecystectomy, 9 cholecystolithotomy and 3 cholecystectomy with splenectomy. CONCLUSIONS: We recommend periodic checks with ultrasound and conservative management is suggested in asymptomatic children. Operative intervention is recommended for symptomatic patients. The surgical treatment of choice in our centre for patients with solitary gallstones and without inflammatory changes in the gallbladder is cholecystolithotomy. We didn't find reappearence of gallbladder after cholecystolithotomy. Laparoscopic cholecystectomy is the best treatment for children with non working gallbladder, "porcelain gallbladder" and in patients with haematologic disease and gallstones.

[Pediatric endoscopy: state of the art]. / Endoscopia: estado actual.

INTRODUCTION: Our society has shown always a great concern with the limits of our speciality. However, we have never approached the issue of pediatric endoscopy. For this reason, we have decided to carry our a survey to assess the present situation of endoscopy among surgeon pediatricians. MATERIAL AND METHODS: Twenty-four hospitals whose services include pediatric surgery were sent a survey centred on the following items: name of hospital, number of beds, in pediatrics, number of surgical interventions per year (which enabled us to classify the services in four groups, depending on their surgical volume), which unit is in charge of esophagus-gastroscopy, colonoscopy, esophageal dilatation, percutaneous endoscopic gastrostomy (PEG), endoscopic retrograde colangio-pancreatography (ERCP), rigid and flexible bronchoscopy, and number of such examinations per year. RESULTS: We received twenty-two answers to the survey (91,88%). The upper endoscopies are carried out in 47,43% of the cases by Pediatric Surgery, (ten units carry out the 100% of the endoscopies in their hospital). All but two ERCP are carry out by the unit of adult gastroenterology, whereas esophageal dilatation and PEG are carry out in 89.33% of cases by Pediatric Surgery. Rigid bronchoscopy is performed by Pediatric Surgery in fifteen units, while flexible bronchoscopy is performed by Pediatric Surgery, Otorhinolaryngology, Pneumology and Pediatrics. CONCLUSIONS: The high degree of response proved the concern with strengthening certain techniques in the field of Pediatric Surgery. Esophageal dilatations and PEG are techniques in the hands of pediatric surgeons, while ERCP is in the hands of adult endoscopists. The units that offer flexible bronchoscopy carry out many more examinations. It would be necessary to reach a consensus regarding various issues related to these examinations, ranging from who is qualified to carry them out to their legal assistance.

[Foreign body aspiration in children]. / Aspiración de cuerpos extraños en la infancia.

The aim to this study is evaluate the history, symptoms, radiographic and endoscopic findings in 420 children who were admitted for suspected foreign body aspiration in our hospital between 1972 and 2005. In 13 children we didn't find foreign body and in 16 children the foreign bodies were lodged in larynx. The mean age was 33 months. The medical history, phisical exploration, auscultation and radiological findings were positive in 91,4%, 78,3%, 91,6% and 81%. The frecuency or foreign body aspiration is undervaluate and sometimes is excluded as diagnosis. Only 218 (51,9%) patients went to the hospital in the first 24 hours, although 87,8% of patients presented symptoms and 75,4% presented severe symptoms. Moreover the removed foreign bodies and suspected foreign bodies are the same in 82,95%. We think that bronchoscopy should by performed in all children who have had a choking episode.