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3.
Eur J Paediatr Neurol ; 20(3): 426-30, 2016 May.
Article in English | MEDLINE | ID: mdl-26943985

ABSTRACT

UNLABELLED: Harlequin syndrome (HS) is a rare autonomic disorder due to a hemifacial cutaneous sympathetic denervation. It is characterized by unilateral diminished sweating and flushing of the face even though after heat or prolonged exercise. It is typically acquired. Congenital cases only represent a 6% of all individuals with HS. All congenital HS cases reported so far showed a concomitant Horner syndrome, probably due to a stellate ganglion involvement. HS represents an uncommon autonomic disorder due to a hemifacial cutaneous sympathetic denervation. It is clinically characterized by a dramatic alteration in facial appearance: ipsilateral denervated pale and dry half from the other intact red and moist half. CONCLUSION: We present, to the best of our knowledge, the first case of a patient with a congenital HS as an isolated phenomenon.


Subject(s)
Autonomic Nervous System Diseases/congenital , Autonomic Nervous System Diseases/diagnosis , Flushing/congenital , Flushing/diagnosis , Hypohidrosis/congenital , Hypohidrosis/diagnosis , Rare Diseases/congenital , Rare Diseases/diagnosis , Face , Humans , Infant , Male
4.
Actas dermo-sifiliogr. (Ed. impr.) ; 104(2): 141-147, mar. 2013. graf, tab
Article in Spanish | IBECS | ID: ibc-109950

ABSTRACT

Objetivo: Analizar las características de las jornadas quirúrgicas dermatológicas y comparar distintos indicadores de rendimiento quirúrgico. Material y método: Estudio descriptivo y retrospectivo de la actividad quirúrgica programada realizada en el Servicio de Dermatología del Hospital Universitario de Fuenlabrada desde enero de 2005 a diciembre de 2010. Se analizan datos relativos a los procedimientos realizados y a las jornadas quirúrgicas. Se analizan los índices de ocupación, de rendimiento quirúrgico mediante tiempos quirúrgicos estándar (TQE) y los valores de adecuación quirúrgica AQ1 y AQ2. La medición de las variables se realiza mediante frecuencias relativas. Se ha calculado la covarianza y el índice de correlación lineal de Pearson entre distintas variables. Resultados: Durante el periodo de estudio se realizaron 11.481 jornadas quirúrgicas. El 71% de las jornadas fueron de cirugía menor y el resto de CMA. La media de pacientes intervenidos/jornada fue de 9,7. El índice global de ocupación de quirófano fue del 71,91%. Cuatro descriptores TQE: «cirugía menor», «lesiones múltiples menores de piel», «cirugía de la uña» y «tumor maligno de piel cierre directo» fueron suficientes para clasificar el 86,7% de las cirugías realizadas. El 91,3% de las intervenciones asociaron un tiempo muerto de TQE 0,15 (9min). La media del indicador AQ1 fue de 1,20. El rendimiento de quirófano global medido mediante el indicador AQ2 fue del 96,46%. El índice de correlación de Pearson mostró relación estadísticamente significativa entre el incremento del número de pacientes/jornada, la disminución del índice de ocupación y el aumento del rendimiento de quirófano AQ2. Conclusiones: La aplicación de los descriptores TQE permite cuantificar la complejidad de los procesos incluidos en LEQ y obtener indicadores para evaluar la actividad quirúrgica, mejorando la eficiencia en la gestión de los tiempos quirúrgicos (AU)


Objectives: To analyze the characteristics of the dermatologic surgery lists and to compare different indicators of surgical productivity. Materials and methods: This was a retrospective, descriptive study of the routine surgical activity undertaken in the Dermatology Department of Fuenlabrada University Hospital, Madrid, Spain, between January 2005 and December 2010. Data about the procedures performed and about the surgical lists were analyzed and an analysis was made of operating room occupancy. Surgical productivity was analyzed using standard operating times (SOTs) and surgical scheduling adequacy values (SA1 and SA2). Variables were recorded as relative frequencies. Covariance and the Pearson linear correlation index were used for comparisons. Results: The study period included a total of 11,481 surgical sessions, of which 71% were minor surgery and the remainder were major outpatient surgery. A mean of 9.7 operations were performed in each session and the overall operating room occupancy was 71.9%. Four SOT descriptors (minor surgery, multiple minor skin lesions, nail surgery, and malignant tumors with primary closure) were sufficient to classify 86.7% of the operations performed. The operating room down-time was 0.15 SOT (9 minutes) in 91.3% of operations. The mean SA1 index was 1.20.Overall surgical productivity measured using the SA2 index was 96.46%. The Pearson correlation showed a statistically significant relationship between the increase in the number of patients persurgical session, the reduction in operating room occupancy, and the increase in SA2 operating room productivity. Conclusions: The application of SOT descriptors enables us to quantify the complexity of the operations included in the surgical waiting list and to obtain indicators for the evaluation of surgical activity, improving efficiency in surgical time management (AU)


Subject(s)
Humans , Surgery Department, Hospital/statistics & numerical data , Skin Diseases/surgery , Time Factors , Quality Indicators, Health Care/statistics & numerical data
5.
Actas dermo-sifiliogr. (Ed. impr.) ; 104(1): 38-43, ene. 2013. graf, tab
Article in Spanish | IBECS | ID: ibc-108471

ABSTRACT

Objetivo: Analizar los datos de pacientes sometidos a cirugía dermatológica en quirófano. Material y método: Estudio descriptivo, retrospectivo, de la actividad quirúrgica programada realizada en quirófano en el Servicio de Dermatología del Hospital Universitario de Fuenlabrada desde enero de 2005 a diciembre de 2010. Se analizan distintas variables relativas al paciente y a la cirugía. La medición de las variables se realiza mediante frecuencias relativas. Se estudian los índices de sustitución y de suspensión, el riesgo proporcional de complicaciones y el rendimiento quirúrgico. Resultados: Durante el periodo de estudio fueron intervenidos 11.516 pacientes, 9.351 en la modalidad de cirugía menor, 1.998 mediante CMA y 167 precisaron cirugía con hospitalización. La patología tratada fue en su gran mayoría de naturaleza benigna (85%) y la escisión simple el procedimiento más realizado (64,7%). El número medio de pacientes/jornada fue de 9,7. El rendimiento quirúrgico medio fue del 71,9%. Conclusiones: El registro adecuado es fundamental para conocer la actividad realizada y poder comparar con otros centros. El análisis evolutivo de los datos registrados permite observar el efecto que las medidas adoptadas tienen sobre los distintos indicadores. En nuestro caso el rendimiento del quirófano en porcentaje de ocupación disminuye al aumentar el número de pacientes intervenidos por jornada (AU)


Objective: To analyze data corresponding to patients who underwent dermatological surgery in an operating room. Material and methods: This was a descriptive, retrospective study of operating room activities in the dermatology department of Hospital Universitario de Fuenlabrada in Madrid between January 2005 and December 2010. We analyzed the relative frequency of a range of patient and procedure-related variables, as well as substitution and cancellation rates, the proportional risk of complications, and operating room efficiency. Results: In the period analyzed, 11 516 patients underwent surgery: 9351 required minor surgery,1998 major ambulatory surgery, and 167 surgery requiring hospitalization. Simple excision was the most common procedure (64.7%), and in the majority of cases (85%), the condition was benign. The mean number of patients treated per day was 9.7, and mean operating room efficiency was 71.9%. Conclusions: Accurate record-keeping is essential for analyzing operating room activities and comparing results with those from other centers. The analysis of patterns over time shows the effect of changes made on different indicators. In our case, a decrease in operating room efficiency was seen with an increase in the number of patients per day undergoing surgery (AU)


Subject(s)
Humans , Skin Diseases/surgery , /statistics & numerical data , Skin Transplantation/statistics & numerical data , Surgery Department, Hospital/statistics & numerical data , Ambulatory Surgical Procedures/statistics & numerical data , Postoperative Complications/epidemiology , Age and Sex Distribution
6.
Actas Dermosifiliogr ; 104(2): 141-7, 2013 Mar.
Article in English, Spanish | MEDLINE | ID: mdl-22944291

ABSTRACT

OBJECTIVES: To analyze the characteristics of the dermatologic surgery lists and to compare different indicators of surgical productivity. MATERIALS AND METHODS: This was a retrospective, descriptive study of the routine surgical activity undertaken in the Dermatology Department of Fuenlabrada University Hospital, Madrid, Spain, between January 2005 and December 2010. Data about the procedures performed and about the surgical lists were analyzed and an analysis was made of operating room occupancy. Surgical productivity was analyzed using standard operating times (SOTs) and surgical scheduling adequacy values (SA1 and SA2). Variables were recorded as relative frequencies. Covariance and the Pearson linear correlation index were used for comparisons. RESULTS: The study period included a total of 11,481 surgical sessions, of which 71% were minor surgery and the remainder were major outpatient surgery. A mean of 9.7 operations were performed in each session and the overall operating room occupancy was 71.9%. Four SOT descriptors (minor surgery, multiple minor skin lesions, nail surgery, and malignant tumors with primary closure) were sufficient to classify 86.7% of the operations performed. The operating room down-time was 0.15 SOT (9minutes) in 91.3% of operations. The mean SA1 index was 1.20. Overall surgical productivity measured using the SA2 index was 96.46%. The Pearson correlation showed a statistically significant relationship between the increase in the number of patients per surgical session, the reduction in operating room occupancy, and the increase in SA2 operating room productivity. CONCLUSIONS: The application of SOT descriptors enables us to quantify the complexity of the operations included in the surgical waiting list and to obtain indicators for the evaluation of surgical activity, improving efficiency in surgical time management.


Subject(s)
Dermatology , Hospital Departments/statistics & numerical data , Operating Rooms/statistics & numerical data , Operative Time , Surgical Procedures, Operative/standards , Hospitals, University , Humans , Operating Rooms/organization & administration , Retrospective Studies , Spain , Time Factors
7.
Actas Dermosifiliogr ; 104(1): 38-43, 2013 Jan.
Article in English, Spanish | MEDLINE | ID: mdl-22831786

ABSTRACT

OBJECTIVE: To analyze data corresponding to patients who underwent dermatological surgery in an operating room. MATERIAL AND METHODS: This was a descriptive, retrospective study of operating room activities in the dermatology department of Hospital Universitario de Fuenlabrada in Madrid between January 2005 and December 2010. We analyzed the relative frequency of a range of patient and procedure-related variables, as well as substitution and cancellation rates, the proportional risk of complications, and operating room efficiency. RESULTS: In the period analyzed, 11,516 patients underwent surgery: 9351 required minor surgery, 1998 major ambulatory surgery, and 167 surgery requiring hospitalization. Simple excision was the most common procedure (64.7%), and in the majority of cases (85%), the condition was benign. The mean number of patients treated per day was 9.7, and mean operating room efficiency was 71.9%. CONCLUSIONS: Accurate record-keeping is essential for analyzing operating room activities and comparing results with those from other centers. The analysis of patterns over time shows the effect of changes made on different indicators. In our case, a decrease in operating room efficiency was seen with an increase in the number of patients per day undergoing surgery.


Subject(s)
Dermatologic Surgical Procedures/statistics & numerical data , Hospitals, University , Operating Rooms , Adolescent , Adult , Aged , Aged, 80 and over , Child , Child, Preschool , Female , Humans , Infant , Male , Middle Aged , Retrospective Studies , Spain , Young Adult
12.
Acta pediatr. esp ; 63(3): 111-113, mar. 2005. ilus
Article in Es | IBECS | ID: ibc-038197

ABSTRACT

El liquen nitidus es una erupción liquenoide que se manifiesta en forma de pápulas brillantes de pequeño tamaño, del color de la piel normal, con carácter asintomático, de forma localizada o generalizada. La confirmación se realiza mediante estudio histopatológico, que presenta un infiltrado linfohistiocitario en dermis superficial con crestas interpapilares elongadas en los bordes abarcando dicho infiltrado. Por su tendencia a la resolución espontánea y la ausencia de síntomas, generalmente no precisa tratamiento


Lichen nitidus is a lichenoid eruption characterized by small, shiny, skin-colored papules. It is asymptomatic and can be localized or generalized. The diagnosis is confirmed by means of histopathological study, which reveals the presence of a lymphohistiocytic infiltrate in the superficial dermis, with elongated interpapillary crests on the borders encircling the infiltrate. Given that it tends to resolve spontaneously and the absence of symptoms, it generally does not require treatment


Subject(s)
Child , Humans , Lichen Nitidus/classification , Lichen Nitidus/physiopathology , Lichenoid Eruptions/etiology , Adrenal Cortex Hormones/administration & dosage , Adrenal Cortex Hormones/adverse effects , Lichen Nitidus/epidemiology , Lichenoid Eruptions/physiopathology , Lichenoid Eruptions/surgery , Histamine H1 Antagonists/administration & dosage , Histamine H1 Antagonists/therapeutic use
13.
Acta pediatr. esp ; 62(10): 473-475, nov. 2004. ilus
Article in Es | IBECS | ID: ibc-36517

ABSTRACT

Malassezia spp. es un género de hongos lipofílicos que tiene relación con la aparición de diversos procesos cutáneos, entre ellos, una forma clínica de foliculitis. La foliculitis por Malassezia presenta unas características clínicas y epidemiológicas que permiten orientar el diagnóstico. La confirmación se realiza fácilmente con la microscopia directa o el estudio histopatológico de alguna de las lesiones. En general, la respuesta a fármacos antifúngicos es buena, aunque las recurrencias son frecuentes por la persistencia de los factores predisponentes (AU)


Subject(s)
Adolescent , Female , Humans , Malassezia/isolation & purification , Folliculitis/microbiology , Folliculitis/diagnosis , Itraconazole/therapeutic use , Antifungal Agents/therapeutic use , Dermatomycoses/drug therapy , Folliculitis/drug therapy
14.
Acta pediatr. esp ; 62(6): 234-236, jun. 2004. ilus
Article in Es | IBECS | ID: ibc-34038

ABSTRACT

La foliculitis pustulosa eosinofílica de la infancia (FPEI) es una dermatosis eosinofílica de etiología desconocida, que se caracteriza por brotes autolimitados de lesiones pustulosas localizadas en el cuero cabelludo desde los primeros meses de vida; no se acompaña de afectación del estado general, y el diagnóstico se basa, de manera fundamental, en el estudio anatomopatológico. Habitualmente, no requiere tratamiento, pero, en caso necesario, se puede pautar la aplicación de corticoides tópicos para mejorar la sintomatología (AU)


Subject(s)
Infant , Humans , Methylprednisolone/therapeutic use , Folliculitis/drug therapy , Folliculitis/pathology , Anti-Inflammatory Agents/therapeutic use
15.
Acta pediatr. esp ; 62(4): 146-148, abr. 2004. tab
Article in Es | IBECS | ID: ibc-32654

ABSTRACT

La morfea en placas es una de las formas cutáneas de la esclerodermia, grupo de trastornos caracterizados por la colagenización y la fibrosis de la piel y otros órganos. Presentamos un caso de morfea en placa localizada en la espalda. Esta forma no es muy frecuente en la infancia y no se asocia a trastornos sistémicos. Los tratamientos no resultan muy eficaces y la enfermedad tiende a evolucionar hacia la curación espontánea (AU)


Subject(s)
Female , Child , Humans , Scleroderma, Localized/diagnosis , Hypergammaglobulinemia/complications , Eosinophilia/complications , Adrenal Cortex Hormones/administration & dosage , Scleroderma, Localized/classification , Scleroderma, Localized/drug therapy
16.
Acta pediatr. esp ; 61(11): 612-613, dic. 2003. ilus
Article in Es | IBECS | ID: ibc-28577

ABSTRACT

Las tiñas inflamatorias son infecciones fúngicas causadas, generalmente, por dermatófitos zoofílicos y geofilicos, que se caracterizan, desde el punto de vista clínico, por la existencia de lesiones con un componente inflamatorio importante de localización variable.Presentamos un caso de tiña inflamatoria del cuero cabelludo (AU)


Subject(s)
Female , Child , Humans , Tinea Capitis/diagnosis , Microsporum/isolation & purification , Tinea Capitis/parasitology , Tinea Capitis/complications , Tinea Capitis/drug therapy , Microsporum/pathogenicity , Alopecia/etiology , Griseofulvin/pharmacology , Prednisone/pharmacology , Chlorhexidine/pharmacology , Arthrodermataceae/pathogenicity , Anti-Bacterial Agents/therapeutic use
19.
Acta pediatr. esp ; 61(6): 296-297, jun. 2003. ilus
Article in Es | IBECS | ID: ibc-24080

ABSTRACT

La infección por el virus del herpes simple neonatal es una enfermedad potencialmente muy grave. Ocurre, en la mayoría de los casos, en el canal del parto, a partir de lesiones activas o de secreciones genitales infectadas. Presentamos un caso infrecuente de adquisición después del Parto, a partir de una localización orolabial materna, con aparición de lesiones limitadas a los dedos de la mano en un lactante de 22 días. El tratamiento correcto y precoz permitió la desaparición total de las lesiones cutáneas y la ausencia de complicaciones asociadas. (AU)


Subject(s)
Male , Humans , Infant, Newborn , Herpes Simplex/pathology , Herpes Simplex/transmission , Herpes Simplex/therapy , Diagnosis, Differential
20.
Acta pediatr. esp ; 60(1): 23-24, ene. 2002. ilus
Article in Es | IBECS | ID: ibc-11054

ABSTRACT

El liquen estriado es un proceso eruptivo intantil que tiene una distribución lineal, se localiza con mayor frecuencia en las extremidades, evoluciona espontáneamente hacia la curación y no se asocia a sintomatología subjetiva importante. La etiología es desconocida, aunque se sospecha que sea viral; no se ha demostrado que sea contagioso y, con mayor frecuencia, se ha observado en pacientes con dermatitis atópica. El diagnóstico se basa en la clínica v la evolución en ocasiones es necesario efectuar una biopsia para diferenciarlo de otros procesos como el nevo epidérmico verrugoso inflamatorio lineal (AU)


Subject(s)
Female , Child, Preschool , Humans , Lichen Planus/diagnosis , Hand Dermatoses/diagnosis , Lichen Planus/pathology , Lichen Planus/drug therapy , Hand Dermatoses/drug therapy , Arm , Vaginal Creams, Foams, and Jellies/administration & dosage , Remission, Spontaneous , Dermatitis, Atopic/diagnosis , Dermatitis, Atopic/drug therapy
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