1.
Pediatrie
; 43(4): 361-70, 1988.
Article
in French
| MEDLINE
| ID: mdl-3419880
ABSTRACT
Seven cases presenting with the features of Byler's disease (BD) are reported. The diagnosis of BD can only be made after exclusion of other causes of cholestasis. It seems likely that BD is a syndrome and that more accurate biological and histological investigations will allow to differentiate several entities within this affection. At the present, liver transplantation appears to be the only rational treatment.
Subject(s)
Cholestasis, Intrahepatic/genetics , Liver Cirrhosis/etiology , Liver/pathology , Child , Child, Preschool , Cholestasis, Intrahepatic/complications , Cholestasis, Intrahepatic/pathology , Female , Humans , Infant , Liver/ultrastructure , Liver Cirrhosis/pathology , Male
2.
Chirurgie
; 103(8): 698-704, 1977 Jun.
Article
in French
| MEDLINE
| ID: mdl-923385