[Peutz-Jeghers syndrome (mucocutaneous melanosis associated with gastrointestinal polyposis). Presentation of 5 cases presenting in the same family]. / Síndrome de Peutz-Jeghers (melanosis mucocutánea asociada a poliposis gastrointenstinal). Presentación de cinco casos pertenecientes a la misma familia.

Five brothers suffering from Peutz-Jeghers syndrome with freckles in the skin of the face and mucous membrane of the oral cavity, and intestinal polyps are reported. These patients have not been traditionally considered of being at risk. The current opinion is that patients with this disorder can develop malignancies in the gastrointestinal tract, and tumors in other organs.

[Plurimucosal cicatricial pemphigoid. A case with involvement of the gingival, vulval and vaginal mucosa]. / Penfigoide cicatrizal plurimucoso. Consideraciones acerca de un cáso con afectación de mucosas gingival, vulvar y vaginal.

We have studied a 62 years old woman with the infrequent involvement of the gingiva (desquamative gingivitis), vulvar and vaginal mucouses in benign mucosal pemphigoid. The clinical features and pathology are exposed and we debate differential diagnosis principally with pemphigus and lichen planus.