ABSTRACT
A 15-year-old boy who presented recurrent bilateral pneumothoraces after allogenic bone marrow transplantation for the treatment of myelodysplastic syndrome is presented. We performed bulla resection under the thoracoscopic surgery for three times. Pathological examination revealed irregular fibrous thickening of the visceral pleura and alveolar fibrosis, consistent with a diagnosis of pleuroparenchymal fibroelastosis (PPFE). Also the findings of bronchiolitis obliterans (BO) was noted and chronic graftversus-host disease( GVHD) was strongly suggested. Twenty-five months after the operation, bilateral living-donor lobar lung transplantation was performed and the diagnosis of GVHD was established.
Subject(s)
Bronchiolitis Obliterans , Graft vs Host Disease , Lung Transplantation , Pneumothorax , Adolescent , Bone Marrow Transplantation/adverse effects , Graft vs Host Disease/complications , Humans , Male , Pneumothorax/diagnostic imaging , Pneumothorax/etiology , Pneumothorax/surgerySubject(s)
Glomus Tumor/diagnostic imaging , Lung Neoplasms/diagnostic imaging , Contrast Media , Diagnosis, Differential , Female , Fluorodeoxyglucose F18 , Glomus Tumor/pathology , Glomus Tumor/surgery , Humans , Lung Neoplasms/pathology , Lung Neoplasms/surgery , Magnetic Resonance Imaging , Middle Aged , Positron-Emission Tomography , Radiographic Image Enhancement , Radiopharmaceuticals , Tomography, X-Ray ComputedABSTRACT
A 59-year-old woman was pointed out isotope uptake at the right pulmonary hilum by positron emission tomography/computed tomography (PET/CT) performed for postoperative follow up of thyroid cancer. Chest enhanced CT showed a mass in the right pulmonary artery, which was diagnosed as sarcoma of pulmonary artery origin by a transcatheter biopsy. Chemotherapy by doxorubicin with anticoagulation therapy was started 1st due to the secondary pulmonary hypertension. Pulmonary hypertension was improved, but the size of the tumor enlarged. She underwent right pneumonectomy with mediastinal dissection. The tumor was completely resected, but brain metastases developed. Postoperative pathological diagnosis was leiomyosarcoma. A rare case of preoperatively diagnosed pulmonary arterial sarcoma was reported.
