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BMJ Case Rep ; 20122012 Nov 19.
Article in English | MEDLINE | ID: mdl-23166163

ABSTRACT

We describe a 17-year-old patient presenting perimyocarditis as the initial manifestation of the adult-onset Still's disease. Corticotherapy was rapidly successful but induced major acute hepatitis in relation with Epstein-Barr virus reactivation. After 1 year, even if the global outcome is favourable, a slightly lowered ejection fraction still persists. Former case reports and differential diagnosis with reactive haemophagocytic syndrome would be discussed.


Subject(s)
Epstein-Barr Virus Infections/diagnosis , Myocarditis/diagnosis , Pericarditis/diagnosis , Still's Disease, Adult-Onset/diagnosis , Virus Activation , Adolescent , Anti-Inflammatory Agents/adverse effects , Anti-Inflammatory Agents/therapeutic use , Chemical and Drug Induced Liver Injury/diagnosis , Diagnosis, Differential , Dose-Response Relationship, Drug , Drug Administration Schedule , Echocardiography , Heart Ventricles/pathology , Humans , Lymphohistiocytosis, Hemophagocytic/diagnosis , Magnetic Resonance Imaging , Male , Myocardium/pathology , Prednisone/adverse effects , Prednisone/therapeutic use , Still's Disease, Adult-Onset/drug therapy
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