[Currarino syndrome--a case report].

The triad of anorectal malformation, a sacrococcygeal defect, and a presacral mass was first described by Kennedy in 1926. Currarino et al recognized these disorders as a syndrome in 1981. The Currarino syndrome (CS) belongs to the group of neurenteric malformations and is associated with chronic constipation. The presacral mass generally is a teratoma or an anterior meningocele. The anorectal malformation either is anal stenosis or agenesis. The 3 anomalies characterizing this syndrome can be ascribed to a common developmental defect or anomaly of the notochord in the early phases of embryogenesis. Currant genetic studies implicate mutations in gene HLXB9 for the autosomal dominant inherited character of the syndrome in about 50% of the patients. A rare case of Currarino syndrome is presented as a first one in our practice with the diagnostic and therapeutic problems and review of the literature.

[A combined posterior sagittal and transabdominal approach for the treatment of children with high type of anal atresia].

The authors present 7 cases (4 girls and 3 boys) with a high type of imperforate anus. Combined posterior sagittal and transabdominal approach was applied. In all 7 cases the height of the malformation, determined by x-ray and ultrasonography was more than 30 mm. One stage surgical procedure, without colostomy, was applied in two of the cases. One child was treated by a two stage and the other four by a three stage operation. The operation is described and the postoperative complications and the results are discussed.

[Surgical treatment of low fistulous forms of anal atresia using postero-sagittal approach in children]. / Operativnoe lechenie nizkikh svishchevykh form atrezii zadnego prokhoda s primeneniem zadnesagittalnogo dostupa u detei.

The problems of surgical treatment of the low fistulous forms of anal atresia in children with the use of postero-sagittal approach are considered. A modification of this method is described. The postoperative results are presented, and the possible complications as well. A conclusion about the advantages of the operative approach described is made.