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Lhermitte-Duclos disease associated with Cowden's disease--case report.

Yuasa, H; Motokishita, T; Tokito, S; Tokunaga, M; Goto, M.

Neurol Med Chir (Tokyo) ; 37(9): 697-700, 1997 Sep.

Article in English | MEDLINE | ID: mdl-9330536

ABSTRACT

A 49-year-old Japanese male with Lhermitte-Duclos disease subsequently developed a very rare association with Cowden's disease. Partial tumor removal established the diagnosis of Lhermitte-Duclos disease. Follow-up examinations discovered the presence of Cowden's disease. Long-term follow-up of patients with Lhermitte-Duclos disease is essential to identify signs of Cowden's disease, which carries the risk of developing malignancy.

Subject(s)

Cerebellar Neoplasms/genetics , Ganglioneuroma/genetics , Hamartoma Syndrome, Multiple/genetics , Cerebellar Neoplasms/pathology , Cerebellar Neoplasms/surgery , Cerebellum/pathology , Cerebellum/surgery , Chromosome Aberrations/genetics , Chromosome Disorders , Endoscopy, Gastrointestinal , Ganglioneuroma/pathology , Ganglioneuroma/surgery , Gastrointestinal Neoplasms/genetics , Gastrointestinal Neoplasms/pathology , Gastrointestinal Neoplasms/surgery , Genes, Dominant/genetics , Hamartoma Syndrome, Multiple/pathology , Hamartoma Syndrome, Multiple/surgery , Humans , Magnetic Resonance Imaging , Male , Middle Aged , Polyps/genetics , Polyps/pathology , Polyps/surgery , Tomography, X-Ray Computed

ABSTRACT

Subject(s)

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