ABSTRACT
INTRODUCTION: Desmoids fibromatosis is a rare pathology whose definitive diagnosis is histological. Although it presents clinical and radiological similarities with breast carcinoma. CASE REPORT: In this observation, we report a case of desmoids fibromatosis diagnosed in a 51-year-old female patient. The positive diagnosis was difficult to retain. DISCUSSION: Desmoids fibromatosis remains a benign pathology with a high recurrence rate and a local aggressiveness requiring an enlarged lumpectomy with sufficient margins up to 3 cm. CONCLUSION: Radiotherapy remains a therapeutic option in addition to surgery in incomplete sections and in case of multiple recurrences. The place of medical treatments, in particular anti-estrogens, is not clearly defined.
