ABSTRACT
Coronary artery fistula is a rare congenital anomaly in which the involved coronary artery empties into a cardiac chamber, pulmonary artery, or other structure. Its diagnosis can be made noninvasively by finding a dilated coronary artery by 2-dimensional (2D) echocardiography, and its drainage can be detected by color flow mapping. We describe features of coronary artery fistulas in 8 patients whose condition was prospectively diagnosed by Doppler echocardiography with color flow mapping. The right coronary artery was involved in 4 cases and the left coronary artery in 4. Four fistulas drained to the right ventricle, 2 to the right atrium, and 2 to the pulmonary artery. In 1 patient who had left and right coronary fistulas to the pulmonary artery, only the first was diagnosed noninvasively. The diagnosis of coronary fistulas can usually be made by 2D echocardiography with color flow mapping. However, fistulas to the pulmonary artery may be more difficult to detect by 2D echocardiography because the coronary artery may be of normal size and the shunt small.
Subject(s)
Coronary Vessel Anomalies/diagnostic imaging , Echocardiography, Doppler , Vascular Fistula/congenital , Vascular Fistula/diagnostic imaging , Adolescent , Adult , Arteries/diagnostic imaging , Child , Child, Preschool , Coronary Vessel Anomalies/physiopathology , Electrocardiography , Female , Humans , Infant , Male , Vascular Fistula/physiopathologyABSTRACT
The case of a 15-month-old patient with Shone's anomaly is reported. This anomaly includes supravalvar mitral ring, parachute mitral valve, subaortic stenosis and coarctation. The patient underwent a corrective surgery with resection of the supravalvar mitral ring, mitral comissurotomy and resection of the subaortic stenosis, anatomically significant lesions, with good postoperative development. A bibliographical review on the anomaly was undertaken.
