Subject(s)
Infant, Newborn , Infant , Humans , Male , Female , Appendicitis , Infant, Newborn, DiseasesABSTRACT
Laryngotracheoesophageal cleft is a rare congenital anomaly that should be considered in the differential diagnosis of any neonatal respiratory distress aggravated by feeding. Diagnosis is difficult, but can be made by roentgenographic and endoscopic techniques. Roentgenographic evidence of abnormal positioning of nasogastric tubes should arouse suspicion. Repeated bronchoscopy may be necessary to identify the defect. Immediate surgical repair is indicated. Incorporation of part of the esophageal wall into the repair may enhance success. Tracheostomy has been required in all survivors. The embryologic pathogenesis of the anomaly is discussed and it is concluded that the defect is found more often than is reported. We present the fifty-fourth case, the first associated to hypospadias in the world, and the first case in the Mexican literature. This child presented severe respiratory distress. Death occurred on the tenth neonatal day.
Subject(s)
Abnormalities, Multiple , Esophagus/abnormalities , Larynx/abnormalities , Trachea/abnormalities , Abnormalities, Multiple/complications , Humans , Hypospadias/complications , Infant, Newborn , Intubation, Intratracheal , Male , Pneumothorax/etiology , Respiratory Insufficiency/etiologyABSTRACT
La hendidura laringotraqueoesofagica es una malformacion congenita rara que debe ser considerada en el diagnostico diferencial de cualquier sindrome de dificultad respiratoria neonatal que se agrave con la alimentacion.El diagnostico es dificil, pero puede lograrse con la ayuda de procedimientos radiograficos y endoscopicos. En el estudio radiografico, la posicion anormal de la sonda nasogastrica debe despertar la sospecha. Pueden ser necesarias broncoscopias repetidas para la identificacion del defecto.La reparacion inmediata es mandatoria. La incorporacion de una parte de la pared esofagica en la linea de sutura puede aumentar las posibilidades de exito. La traqueotomia ha sido una maniobra necesaria en todos los pacientes que han sobrevivido. Se discute la embriologia del defecto y ser mas comun de lo referido en la literatura. Presentamos el caso numero 54, el primero asociado reportado en Mexico. Este paciente presento signos graves de insuficiencia respiratoria y la muerte ocurrio al decimo dia de vida
