ABSTRACT
Papulosis of the scapular areas is a characteristic dermatologic sign of Hunter's disease. It has not been described in the other mucopolysaccharidoses. This sign had been detailed by Hunter in 1917 in his princeps observation. We noted it in two cases of the disease. The ultrastructural study showed an accumulation in the connective interstitial substance of anhist bodies of intra-cellular origin.
Subject(s)
Connective Tissue/pathology , Mucopolysaccharidosis II , Mucopolysaccharidosis II/pathology , Child , Humans , Male , Mucopolysaccharidosis II/genetics , PedigreeSubject(s)
Shoulder Dislocation/surgery , Arthrodesis , Female , Follow-Up Studies , Humans , Male , Middle AgedABSTRACT
The authors have treated 50 cases of non specific spondylitis in adults and reviewed the clinical signs and diagnostic problems in this condition. They advocate a systematic surgical approach to the focus. This allows identification of the organism unless the patient has previously received antibiotics. Even then, a direct approach allows histological examinations to be made and necrotic and infected tissues to be cleaned up. In 12 highly destructive lesions, a bone graft was added. The results were more satisfactory when fusion across the disc was achieved. There were only two deaths.
Subject(s)
Bacterial Infections , Spondylitis , Adolescent , Adult , Aged , Anti-Bacterial Agents/therapeutic use , Bacterial Infections/diagnosis , Diagnosis, Differential , Female , Follow-Up Studies , Humans , Iatrogenic Disease , Immobilization , Male , Middle Aged , Radiography , Spinal Fusion , Spine/diagnostic imaging , Spondylitis/diagnosis , Spondylitis/etiology , Spondylitis/therapy , Surgical Wound Infection , Tuberculosis, Spinal/diagnosisABSTRACT
The authors have studied 62 cases of aplasia of hypoplasia of the fibula. They note that developmental abnormalities affect the whole of the lower limb. They describe the evolution of the bony deformities and of anomalies of the soft tissues. They conclude that discrepancy in limb length is the major factor in the prognosis and that it increases uniformally. Surgery is indicated even when a definitive prosthesis is planned. The possibility of leg lengthening must be approached with caution.
Subject(s)
Bone Diseases, Developmental , Fibula/abnormalities , Adolescent , Artificial Limbs , Bone Diseases, Developmental/surgery , Bone Lengthening , Child , Child, Preschool , Female , Humans , Infant , Leg Length Inequality , MaleSubject(s)
Arm/blood supply , Arteries/injuries , Ischemia/surgery , Leg/blood supply , Adolescent , Adult , Aged , Arteries/surgery , Female , Humans , Male , Middle AgedABSTRACT
Based on the analysis of 45 cases of comminuted fractures of the lower extremity of the radius, this study points out the insufficiency of conventional treatments. The authors advocate a technique using a Kirschner's wire passed through the metacarpal bones and another one through the ulna, both beind embeded in plaster cast. This method was tested on 19 cases with encouraging results. The technique was precisely described and the authors think that it should be used in fractures incorrectly reduced by conventional methods.
