ABSTRACT
The history and clinical findings of 30-year man with Alport's syndrome are presented. The main features of Alport's syndrome are hereditary chronic nephritis leading to renal failure resulting in death and sensory-neural deafness. Ocular features include anterior lenticonus, macular and peripheral flecks resembling fundus albipunctatus. The etiology of this syndrome is unknown. It has been suggested that there may be a metabolic defect in the biosynthesis of collagen with changes in the glomerular basement membrane, cochlea and capsule of the lens. The retinal flecks may also be related to the different underlying glial cells, Mullers cells producing thick basement membrane. It is concluded that diagnosis of fundus albipunctatus should not be made in the absence of full renal investigation and audiometry.
Subject(s)
Nephritis, Hereditary , Retina/pathology , Adult , Fundus Oculi , Humans , Male , Nephritis, Hereditary/diagnosis , OphthalmoscopyABSTRACT
PURPOSE: Intra-operative and postoperative complications of the first 50 phacoemulsifications were evaluated. The procedures were performed by one, skilled at ECCE surgeon. The phaco-chop technique was carried out in all cases with use of anterior chamber maintainer (ACM). MATERIAL AND METHODS: Eyes for surgery met the requirements: normal comea, presence of red reflex from the fundus and correct lens position. The patients were divided into 2 groups: I group--25 eyes had first surgery, II group--25 eyes had second surgery. On the first day after surgery complications and uncorrected acuity were evaluated. RESULTS: 50 eyes of 48 patients underwent operation. The mean age was 69.4 years 5% eyes had previous surgical record: 4--underwent trabeculectomy, 1--pars plana vitrectomy. The 12 intra-operative complications appeared in 10 eyes (20%): posterior capsule rupture without vitreous loss in 4% and 10% with vitreous loss, Descemet membrane detachment in 4%, iris dialysis in 2%, and persistent iris damage without sphincter disruption in 4%. The 16 postoperative complications concerned 10 eyes (20%): corneal oedema in 20%, transient intra-ocular pressure raise in 8%, hyphaema in 2%, and fibrin exudation in 2%. The majority of complications concerned the I group of eyes. The uncorrected visual acuity was 0.5 or better in 80% of eyes, on the first day after the operation. CONCLUSIONS: The use of ACM made the first steps in phacoemulsification rate during the learning course.
Subject(s)
Clinical Competence , Intraoperative Complications/etiology , Phacoemulsification/adverse effects , Phacoemulsification/education , Postoperative Complications/etiology , Aged , Female , Humans , Learning , Male , Phacoemulsification/methods , Reoperation , Treatment Outcome , Visual AcuityABSTRACT
Two cases of the long term observation and clinical findings of choroidal osteoma are presented. Choroidal osteoma (choroidal osseous choristoma) is a very rare, benign, ossifying tumour of the choroid, which typically affects healthy young women. The etiology is unknown. Neovascularisation and haemorrhage is a frequent associated finding. Subretinal neovascularisation, which tend to develop progressive visual loss, may be treated successfully with argon or krypton laser photocoagulation.
