ABSTRACT
We describe two infants with congenital myotonic dystrophy that was complicated by persistent pulmonary hypertension. Both infants died of respiratory insufficiency that was unresponsive to ventilatory and pharmacologic support. One of the two infants was supported with extracorporeal membrane oxygenation before the diagnosis of congenital myotonic dystrophy was made.
Subject(s)
Myotonic Dystrophy/congenital , Persistent Fetal Circulation Syndrome/complications , Extracorporeal Membrane Oxygenation , Fatal Outcome , Female , Humans , Infant, Newborn , Male , Myotonic Dystrophy/complications , Myotonic Dystrophy/diagnosis , Persistent Fetal Circulation Syndrome/therapyABSTRACT
We describe two infants with congenital diaphragmatic hernia who underwent extracorporeal membrane oxygenation and in whom the venous cannula was in the left atrium instead of the right. The routine radiograph of the chest failed to demonstrate the malposition. We recommend using the echocardiogram to confirm the position of the cannula or to guide the surgeon during the cannulation of patients with congenital diaphragmatic hernia.