ABSTRACT
Rosai-Dorfman disease (RDD) is a rare benign proliferative histiocytic disorder characterised by massive lymphadenopathy. While extranodal involvement can occur in generalised RDD, isolated soft tissue RDD (STRDD) is extremely rare. We report a 17-year-old male patient who presented to the maxillofacial outpatient department of the Sultan Qaboos Hospital, Salalah, Oman, in 2015 with a painless cheek mass which had been slowly growing over the previous two months. Routine histopathological examinations and immunohistochemistry confirmed a diagnosis of STRDD. Currently, surgical excision is considered to be the most effective curative treatment for STRDD, as the outcomes of other treatment modalities are still unknown. Despite its rarity, STRDD should be considered in the differential diagnosis of histiocytic soft tissue lesions.
Subject(s)
Cheek/abnormalities , Histiocytosis, Sinus/complications , Adolescent , Cheek/surgery , Histiocytosis, Sinus/diagnosis , Humans , Lymphadenopathy/complications , Lymphadenopathy/diagnosis , Male , Oman , Treatment OutcomeABSTRACT
Syringocystadenomapapilliferum is an extremely rare benign adnexal tumor of the scalp and face region. This is a report of the case of a female patient with syringocystadenomapapilliferum originating from the bony cartilaginous junction of the external auditory canal. A provisional diagnosis of an inflammatory polyp was made based on the clinical and radiological findings. Diagnosis was established only after the histopathological examination. This article represents a report of a rare skin disease and a rare site of affection. It emphasizes the role of histopathology in the diagnosis of such a condition with debatable clinical and radiological findings.
