Subject(s)
Catecholamines/metabolism , Ear Neoplasms/metabolism , Paraganglioma/metabolism , Tympanic Membrane , Humans , Male , Middle AgedSubject(s)
Humans , Male , Middle Aged , Catecholamines , Ear Neoplasms , Paraganglioma , Tympanic MembraneABSTRACT
Congenital hypopituitarism due to pituitary stalk and anterior pituitary hypoplasia accompanied by an ectopic posterior pituitary lobe is a rare disorder causing multiple hormone deficiencies. Clinical signs can be present at birth (hypoglycemia, prolonged jaundice and micropenis) and there can be severe growth restriction. Therefore, diagnosis is usually performed in childhood. We present the uncommon case of a 67-year-old man with hypopituitarism due to hypoplasia of the anterior pituitary and pituitary stalk together with an ectopic posterior pituitary who presented symptoms of hyponatremia due to adrenocorticotropic hormone deficiency.
Subject(s)
Brain Diseases/complications , Choristoma/complications , Hypopituitarism/etiology , Pituitary Gland, Anterior/abnormalities , Pituitary Gland, Posterior , Age of Onset , Aged , Brain Diseases/diagnosis , Brain Diseases/pathology , Choristoma/diagnosis , Choristoma/pathology , Craniocerebral Trauma/complications , Depressive Disorder/complications , Dwarfism, Pituitary/etiology , Hormone Replacement Therapy , Humans , Hypopituitarism/drug therapy , Hypopituitarism/epidemiology , MaleABSTRACT
El hipopituitarismo congénito por hipoplasia conjunta de tallo hipofisario e hipófisis anterior acompañada de neurohipófisis ectópica es un trastorno raro que causa múltiples deficiencias en la producción de hormonas. Todo ello puede conducir a signos clínicos en el momento del nacimiento (hipoglucemia, ictericia prolongada y micropene) y retraso severo del crecimiento. Por lo tanto, su diagnóstico se realiza habitualmente en edad infantil. Aquí presentamos un raro caso de un paciente de 67 años de edad con hipopituitarismo por una hipoplasia de la hipófisis anterior y el tallo hipofisario, junto con neurohipófisis ectópica diagnosticado por clínica de hiponatremia, debido a una deficiencia de corticotropina (ACTH)(AU)
Congenital hypopituitarism due to pituitary stalk and anterior pituitary hypoplasia accompanied by an ectopic posterior pituitary lobe is a rare disorder causing multiple hormone deficiencies. Clinical signs can be present at birth (hypoglycemia, prolonged jaundice and micropenis) and there can be severe growth restriction. Therefore, diagnosis is usually performed in childhood. We present the uncommon case of a 67- year-old man with hypopituitarism due to hypoplasia of the anterior pituitary and pituitary stalk together with an ectopic posterior pituitary who presented symptoms of hyponatremia due to adrenocorticotropic hormone deficiency(AU)
