ABSTRACT
Nonorganic hearing loss in children can result from many factors. It is possible that some children show nonorganic hearing loss because of the stresses of past or on-going abuse and neglect. We report three cases of nonorganic hearing loss in children with a history of abuse. These cases suggest that among other causes, child abuse or neglect is to be ruled out when a child shows false hearing loss. Discussions with professionals knowledgeable of a child's home life should be a initiated when nonorganic pediatric hearing loss is uncovered.
Subject(s)
Child Abuse , Hearing Loss, Sensorineural/etiology , Hearing Loss/etiology , Adolescent , Audiometry, Pure-Tone , Hearing Loss/diagnosis , Hearing Loss, Sensorineural/diagnosis , Humans , MaleSubject(s)
Audiology/methods , Correction of Hearing Impairment , Deafness/rehabilitation , Auditory Perception , Child, Preschool , Female , Humans , Infant , Language Development , Male , Sign LanguageABSTRACT
Audiologic evaluations and impedance audiometry were obtained on persons from 13 families with dominant osteogenesis imperfecta (OI). Hearing impairment appeared in the late second or early third decade, usually with a conductive loss. Older patients had mixed or sensorineural losses. There was an increasing risk for hearing loss with advancing age. Impedance tests suggested that ossicular fixation may be the primary cause of middle ear disorders in patients with mixed or conductive hearing losses. The cause of sensorineural hearing loss could not be determined. The long-term success of otologic surgery in OI is uncertain. Amplification may be a reasonable alterative to surgery.
Subject(s)
Hearing Loss/etiology , Hearing , Osteogenesis Imperfecta/physiopathology , Acoustic Impedance Tests , Adolescent , Adult , Aged , Child , Child, Preschool , Female , Hearing Loss/surgery , Humans , Male , Middle Aged , Osteogenesis Imperfecta/complications , Stapes SurgeryABSTRACT
Retinal abnormalities associated with hearing loss may be inherited alone or with additional manifestations. Environmental insults, such as rubella embryopathy, may also cause these abnormalities. We studied 13 patients with retinal abnormalities and hearing loss. Five had Usher's syndrome (retinitis pigmentosa and hearing impairment), one had crystalline retinopathy, two had associated enamel dysplasias, two had clumped pigmentary retinopathy, and three had Amalric-Diallinas syndrome. Our findings suggest considerable heterogeneity of syndromes involving retinal abnormalities and hearing loss.
Subject(s)
Hearing Loss/complications , Retinal Degeneration/complications , Retinitis Pigmentosa/complications , Adolescent , Adult , Child , Child, Preschool , Dental Enamel Hypoplasia/complications , Female , Hearing Loss/genetics , Humans , Infant , Infant, Newborn , Male , Middle Aged , Pregnancy , Retinal Degeneration/genetics , Retinitis Pigmentosa/genetics , SyndromeABSTRACT
Evaluation of hearing acuity at 3000 Hz may be required when there is claim of financial compensation for hearing loss. If collapsing pinnea or ear canals are present, circumaural ear cushions on audiometer earphones can be used to avoid spurious elevation of thresholds. A dial correction is developed for application at 3000 Hz, to be used with corrections developed in a previous study when NAF-48490-1 circumaural ear cushions are used during audiometry.
Subject(s)
Audiometry, Pure-Tone/instrumentation , Audiometry/instrumentation , Adult , Disability Evaluation , Hearing Loss/diagnosis , Humans , Middle AgedABSTRACT
Classroom hearing aid and earmold inspection of the amplification worn by 109 school-age children was performed by an audiologist. Hearing aids and earmolds were classified as adequate or inadequate depending on whether optimal function of the hearing aids and good fit of the earmolds was found. Over 60% of the children were found to be using malfunctioning hearing aids or poorly fitting earmolds. The large number of children wearing inadequate amplification demonstrates the need for constant hearing aid monitoring and earmold check as part of aural rehabilitation and educational programs for hearing-impaired children. A method for accomplishing hearing aid and earmold check by parents and school personnel is described.
Subject(s)
Education, Special , Hearing Aids/instrumentation , Hearing Loss/rehabilitation , Amplifiers, Electronic , Child , Evaluation Studies as Topic , Humans , Maryland , MethodsABSTRACT
The hearing status of 18 patients with Morquio's syndrome (mucopolysaccharidosis IV) was evaluated. All three patients under age 8 years had a conductive hearing loss. Fourteen of 15 patients 8 years of age and older had a mixed or sensorineural hearing loss; one had normal hearing. Six patients wore hearing aids. By the end of the first decade of life, most persons with Morquio's syndrome may be expected to have either a mixed or sensorineural hearing loss. Amplification may be required.
