ABSTRACT
Subarachnoid hemorrhage (SAH) due to sickle-cell anemia is rare, but potentially devastating. However, with early recognition of SAH, aggressive support with exchange transfusion, cerebral angiography, and neurosurgical intervention, a positive outcome may be achieved. A case report of SAH managed in this fashion is reported. Based on similar cases in the literature, a suggested treatment protocol is provided for the management of nontraumatic SAH in sickle-cell patients presenting to the ED.
Subject(s)
Anemia, Sickle Cell/complications , Intracranial Aneurysm/complications , Subarachnoid Hemorrhage/etiology , Subarachnoid Hemorrhage/surgery , Adult , Cerebral Angiography , Clinical Protocols , Combined Modality Therapy , Emergency Medicine , Exchange Transfusion, Whole Blood , Female , Humans , Subarachnoid Hemorrhage/diagnostic imaging , Tomography, X-Ray ComputedABSTRACT
We report on a male infant with an unusual type of acrocephalosyndactyly presenting with unilateral coronal craniosynostosis, cutaneous syndactyly of toes 2 and 3, loss of distal triradii, and transverse alignment of dermal ridges of the palm suggesting syndactyly, atresia of the proximal jejunum, and anal stenosis.