ABSTRACT
Pulmonary artery sarcomas are exceptionally unusual. Their clinic, diagnosis and treatment play a very important role in the ultimate outcome and long-term survival. We present the case of a 70-year-old gentleman diagnosed with a leiomyosarcoma of the pulmonary artery with osteosarcoma differentiation that underwent surgical resection and subsequent chemotherapy, with good recovery at 9 months follow-up. Late diagnosis and incomplete surgical resection will worsen the short- and long-term prognosis of these patients.
Subject(s)
Bone Neoplasms , Leiomyosarcoma , Lung Neoplasms , Osteosarcoma , Sarcoma , Aged , Bone Neoplasms/diagnostic imaging , Bone Neoplasms/pathology , Bone Neoplasms/surgery , Humans , Leiomyosarcoma/diagnostic imaging , Leiomyosarcoma/pathology , Leiomyosarcoma/surgery , Lung Neoplasms/pathology , Male , Osteosarcoma/pathology , Osteosarcoma/surgery , Pulmonary Artery/diagnostic imaging , Pulmonary Artery/pathology , Pulmonary Artery/surgery , Sarcoma/pathology , Sarcoma/surgeryABSTRACT
We present the case of a 37-years old male, who consulted for an extended history of intermittent nausea and vomiting. Laboratory tests showed moderate elevated bilirubin (1.30 mg/dL) and GGT (106 U/L). An abdominal CT scan performed showed a solid 18-centimetres (cm) mass located in the right liver lobe. A biopsy of the lesion was performed, revealing metastastic cells of a well-differentiated neuroendocrine tumour (NET, G3 (Ki-67: 25%). Further study was performed with MRI, and SPECT-CT, showing a 2-cm lesion in the pancreatic tail suggestive of being the primary NET. Chromogranin A levels were high (114.100 ng/ml). In our case, despite the large size of the liver metastasis a full resection of the tumours was achieved.
