Solid pseudopapillary pancreatic tumor as a portal hypertension causal: the first reported case in Puerto Rico.

We describe the first reported case in Puerto Rico of Solid Pseudopapillary Tumor (SPT) of the pancreas causing portal hypertension. Clinical presentation and characteristic imaging findings are helpful to differentiate SPT from pancreatic carcinoma. Diagnosis can be confirmed by histopathological and immunohistochemical approach through biopsy. Timely surgical intervention can prevent portal hypertension as manifestation and be lifesaving in case of malignant degeneration, giving the patient an excellent prognosis after tumor surgical resection.