Orofacial findings and dental management of Williams-Beuren syndrome.

Williams-Beuren syndrome is a rare congenital disorder involving the cardiovascular system, mental retardation, distinctive facial features, and tooth anomalies. The aim of the present report is to show a 10-year-old girl with Williams-Beuren syndrome, her general and orofacial clinical characteristics and the dental management.

Manifestaciones orales y manejo de un paciente pediátrico con esclerodermia localizada: revisión de literatura y reporte de un caso / Oral manifestations and management of localized scleroderma in childhood: Review of the literature and case report

La esclerodermia es una rara enfermedad que afecta los tejidos de origen mesenquimatoso y ectodérmico. Se caracteriza por la aparición de alteraciones inflamatorias y vasculares, además de esclerosis en la piel y órganos de los sistemas respiratorio, cardiovascular y gastrointestinal. El propósito del presente reporte es describir el caso de una niña de 4 años con esclerodermia localizada, sus manifestaciones clínicas, datos epidemiológicos y sugerencias de manejo odontológico de los pacientes pediátricos con esta rara enfermedad.

Scleroderma is a rare disorder that affects mesenchymal and ectodermal tissues. It is characterized of vascular and inflammatory alterations and sclerosis in the skin and organs of respiratory, cardiovascular and gastrointestinal systems. The purpose of this report is to describe the case of a 4 year old girl with localized scleroderma, its clinical manifestations, epidemiological data and recommendations of dental management for the pediatric patients with this rare disease.

Orocraniofacial findings and dental management of a pediatric patient with Dubowitz syndrome.

Dubowitz syndrome is a rare genetic condition characterized by microcephaly, dysmorphic facial features and delayed general growth. It is transmitted through autosomal recessive inheritance. The purpose of this report is to describe the oral, craniofacial and systemic characteristics of a 7-year 11-month-old boy with Dubowitz syndrome and the dental management provided. The pediatric dentist should possess the ability to recognize this rare alteration, to provide dental treatment and to refer for the necessary medical and multidisciplinary treatment.

Intraoral findings and other developmental conditions in Mexican neonates.

PURPOSE: The objective of this study was to investigate the prevalence of intraoral findings and other minor developmental malformations in newborns from San Luis Potosi, Mexico. METHODS: Study subjects were neonates born in San Luis Potosi Morones Prieto Hospital between September 1989 and February 1990. All subjects are examined at this hospital within 20 hours of birth. Premature babies or those requiring intensive care were excluded. Examinations are performed by a team consisting of a geneticist, an oral pathologist, 2 dentists, and an oral surgeon using mirrors, tongue blades, and a flashlight. RESULTS: The team examined 2,182 neonates and found a frequency of 99% for congenital oral cysts, 2% for natal teeth, 11% for ankyloglossia, 8% for commissural lip pits, and 54% for congenital vascular malformations. The male/female ratios for ankyloglossia and natal teeth were 1.5:1 and 1:2.3, respectively. CONCLUSIONS: Babies born at the same hospital demonstrated a high rate of oral cysts, natal teeth, ankyloglossia, and commissural lip pits.

Cytomegalovirus excretion in children attending day-care centers.

BACKGROUND: Healthy children attending day-care centers (DCC) may excrete cytomegalovirus (CMV) frequently. Mothers of children excreting CMV are at higher risk for acquiring this infection than mothers of children not excreting CMV. Despite the increased attendance to DCC by children there is a lack of information regarding CMV infection in Mexico. METHODS: Prospective determination of CMV excretion in saliva of children attending public and private DCC. Three saliva samples were collected during a 2-month follow-up period from participating children and the presence of CMV was determined by viral culture. Demographic features of children and DCC type were taken into account when comparing children with and without CMV excretion. RESULTS: One hundred fifty-two children participated in the study (84 from public and 68 from private DCC). Overall, 17 (11.2%) children excreted CMV during the study period. Excretion rates varied between DCC from 3.1 to 31.3%. Children from private DCC were as likely to excrete CMV as children from public DCC. There were no demographic or clinical features of children associated with viral excretion. CONCLUSIONS: CMV was excreted on an average of 11.2% children attending DCC. The type of DCC or other demographic features were not associated with the likelihood of CMV excretion. CMV seronegative mothers of children who attend DCC need to be aware of the possibility of CMV acquisition and transmission in DCC.