[Epidemiology and clinical polymorphism of the humero-scapulo-facial form of progressive muscular dystrophy]. / Epidemiologiia i klinicheskii polimorfizm plechelopatochnolitsevoi formy progressiruiushchei myshechnoi distrofii.

The paper is concerned with a clinico-genealogic analysis of 9 patients with the humeroscapular form of Landouzy-Dejerine myodystrophy. The patients come from 4 families united by the common ancestor. The following aspects of the illness are marked: a mild course and considerable clinical polymorphism manifesting itself in the age difference by the disease onset as well as in the intensity of the clinical symptoms. These characteristics are of practical importance for regional medicogenetic counselling.