ABSTRACT
Respiratory insufficiency is the clinical principal sign of cystic pulmonary lymphangiectasis. Clarification of cardiovascular morphology and haemodynamics is the basic prerequisite for the classification and therapy of the disease pattern. The prognosis is unfavourable if it is found that the pulmonary circulation does not flow through the lungs, reaching instead the systemic circulation via the persisting ductus arteriosus. The histopathological findings as well as the results of dissection of the cardiovascular system clarify the question as to the pathogenesis of this disease and allow subdivision of the disease into a primary and a secondary manifestation of cystic pulmonary lymphangiectasis.
Subject(s)
Hemodynamics , Lung Diseases/congenital , Lymphangiectasis/congenital , Ductus Arteriosus, Patent/complications , Humans , Infant, Newborn , Lung Diseases/complications , Lung Diseases/diagnosis , Lymphangiectasis/complications , Lymphangiectasis/diagnosis , Male , Prognosis , Respiratory Insufficiency/etiologyABSTRACT
Axial oblique views were performed during cineangiography of congenital heart disease on patients of a paediatric cardiological unit for a period of two years. The resulting angle-patterns are shown in a synoptical review, and indications for angiographic demonstration of morphological conditions in congenital heart disease are discussed. In comparison with the literature to date, this is the first report of experience with a biplane synchronised "C" arm cineangiographic system.
Subject(s)
Cineangiography , Heart Defects, Congenital/diagnostic imaging , Child , HumansABSTRACT
Report on a cardiologic study conducted in 26 juvenile diabetics with insulin deficiency, in whom the disease had lasted for more than ten years. Electrocardiograms, vectorcardiograms and echocardiograms were recorded. The investigations did not indicate the presence of a subclinical cardiomyopathy as a sign of an early diabetic microangiopathy of the myocardium. Hence the findings by Riff and Riff (1974) as well as those by Sanderson et al (1978) have not been confirmed.
Subject(s)
Diabetes Mellitus, Type 1/complications , Heart Diseases/complications , Adolescent , Adult , Diabetes Mellitus, Type 1/diagnosis , Echocardiography , Electrocardiography , Female , Heart Diseases/diagnosis , Humans , Male , VectorcardiographyABSTRACT
To diagnose a possible latent or manifested cardiomyopathy, 143 male patients between 2 and 21 years of age with confirmed Duchenne muscular dystrophy were examined for serum enzymes, by electrocardiography, vector-cardiography, and echo-cardiography. The results contain information on 1. the quantitative cellular myocardial degeneration process, 2. the disturbed cellular depolarization and nerve-conduction processes in the area of the right and left ventricular myocard, and 3. the disturbed left ventricular function which, in the initial state, is only documented by a discrete decrease of contractility caused by a manifested decreased ejection output. The pathological contraction and relaxation process of the heart muscle cell and its dependency on calcium ion transport as pathogenic background is discussed.
