Primary sarcoma of the pancreas, a rare histopathological entity. A case report with review of literature.

AIMS: primary pancreatic sarcomas represent an extremely rare histopathological entity accounting for less than 0.1% of all pancreatic malignancies. Pancreatic sarcomas tend to be more aggressive and have a poor prognosis. METHODS: the case of a 52 year old patient presenting with jaundice is presented and the available literature was reviewed. RESULTS: primary pancreatic sarcomas are extremely rare. Pancreatic sarcomas are more aggressive than other pancreatic neoplasms. CONCLUSION: primary sarcomas of the pancreas are extremely rare, are aggressive and are associated with very poor prognosis.