ABSTRACT
Glial choristoma is a developmental malformation of heterotopic central nervous tissue with limited growth potential. It is considered to be one of the very rare choristomatous lesions involving the oral cavity. This report details the morphological characteristics of glial choristoma arising from the palate in a newborn. Bulk of the tissue comprised of mature neuroglial tissue with astrocytes representing developing brain, cystic spaces lined by cuboidal epithelium indicating ependymal layer. Clinical features, associated malformations and histomorphology of this lesion is discussed.
Subject(s)
Brain , Choristoma/diagnosis , Mouth Diseases/diagnosis , Neuroglia , Choristoma/pathology , Choristoma/surgery , Diagnosis, Differential , Female , Humans , Infant, Newborn , Mouth Diseases/pathology , Mouth Diseases/surgeryABSTRACT
Klippel Trenaunay syndrome is a rare congenital disorder characterised by vascular anomalies and life threatening complications. Clinical recognition, prenatal diagnosis and counselling is important in these cases. Here we present a case of Klippel-Trenaunay syndrome and emphasize upon the clinical significance of such cases.
Subject(s)
Fetal Diseases , Klippel-Trenaunay-Weber Syndrome/congenital , Autopsy , Fetal Diseases/pathology , Humans , Klippel-Trenaunay-Weber Syndrome/pathology , MaleABSTRACT
A case of ganglioneuroma presenting as a retroperitoneal mass in a 5-yr-old girl was diagnosed by preoperative fine-needle aspiration cytology. The cytologic smears predominantly showed clusters of Schwann cells, with scattered mature ganglion cells. The cytologic diagnosis of ganglioneuroma was subsequently confirmed on histopathologic examination. To date, very few reports on the cytologic features of this tumor exist. The importance of considering a confident diagnosis by cytology, and of the uncommon age group that may be affected, is stressed. Diagn. Cytopathol. 1999;21:194-196.
